RESUMO
The Vogt-Kayanagi-Harada ssyndrome in two negro female patients with 37 and 40 year-old, respectively, are reported. The clinic, epidemiologic, heredo-familial and immunologic aspects are discussed.
Assuntos
Uveíte , Síndrome Uveomeningoencefálica , Adulto , Albuminas/líquido cefalorraquidiano , Feminino , Globulinas/líquido cefalorraquidiano , Humanos , Pré-Albumina/líquido cefalorraquidiano , Albumina Sérica/análise , Soroglobulinas/análise , Síndrome , Uveíte/sangue , Uveíte/líquido cefalorraquidiano , Síndrome Uveomeningoencefálica/sangue , Síndrome Uveomeningoencefálica/líquido cefalorraquidianoRESUMO
Os autores relatam a sindrome de Vogt-Koyanagi-Harada em duas mulheres adultas e de cor parda. Sao discutidos os aspectos clinicos, epidemiologicos, heredofamiliares e imunologicos
Assuntos
Transtornos da Pigmentação , Uveíte , Síndrome UveomeningoencefálicaRESUMO
A young woman with acute intermittent porphyria in profound relapse and severe nervous and respiratory involvement was treated by intravenous infusions of hematin, followed by improvement of symptoms. The diet with high carbohydrate and protein content and a B-adrenergic blocking agent, not showed any beneficial effect on acute attack. The infusion of hematin was followed by a lowering effect on urine porphybilinogen and delta-aminolevulinic acid and clinical improvement. The return to normal of porphyrin precursors in the urine was accompanied by almost complete clinical remission. The relationship of remission and repression of delta-aminolevulinic acid, decrease of urinary levels of porphyrin precursors, pulmonaries tests and electromyograms, were discussed.
