Inferior vena cava hypoplasia with right hepatic vein and accessory inferior hepatic vein shunt.

Inferior vena cava (IVC) hypoplasia is a rare condition. Venous blood flow is usually provided through collaterals in the azygos or hemiazygos venous systems. However, portosystemic shunts with intrahepatic venous collateral are extremely rare. The case is presented here of a large shunt between the right hepatic vein, accessory inferior hepatic vein, and inferior vena cava in a 37-year-old female patient with IVC hypoplasia.