RESUMO
We report an intrahepatic portosystemic venous shunt (IPVS) detected by ultrasound in an asymptomatic newborn. The lesion, which was further documented using color Doppler ultrasound and magnetic resonance imaging (MRI), had almost totally disappeared 6 months later without any treatment. Intrahepatic portosystemic venous shunts (IPVS) are uncommon and their etiology is controversial. Some cases of IPVS have been reported in the literature, most of them in adult patients with portal hypertension and cirrhosis of the liver. However, only scattered reports describe IPVS in the absence of liver pathology. A revision of the proposed etiologies of IPVS is made and the usefulness of gray-scale and color Doppler sonography and MRI in diagnosing IPVS is discussed.
Assuntos
Fístula/congênito , Veias Hepáticas/anormalidades , Imageamento por Ressonância Magnética , Veia Porta/anormalidades , Ultrassonografia Doppler em Cores , Veia Cava Inferior/anormalidades , Fístula/diagnóstico por imagem , Seguimentos , Veias Hepáticas/diagnóstico por imagem , Humanos , Recém-Nascido , Masculino , Veia Porta/diagnóstico por imagem , Radiografia , Veia Cava Inferior/diagnóstico por imagemRESUMO
The purpose of this article is to present a case of juvenile xanthogranuloma with pulmonary, retroperitoneal and splenic involvement. The similar echographic pattern of the cutaneous and visceral lesions was very helpful in order to suggest the correct diagnosis.
Assuntos
Xantogranuloma Juvenil/congênito , Abdome/diagnóstico por imagem , Feminino , Humanos , Recém-Nascido , Radiografia Torácica , Ultrassonografia , Xantogranuloma Juvenil/diagnóstico por imagemRESUMO
A premature infant with nonbacterial endocardial thrombosis and embolization of the cerebral circulation is presented. The patient was born at 32 weeks with a birthweight of 1480 g. Pregnancy was complicated by toxemia and placental infarctions. Echocardiographic examination by 12 hours after birth revealed a large mass in the right atrium compatible with endocardial thrombus. Follow-up echocardiograms showed a small mass in the left atrium and a decrease of the right atrial mass by day 7. Echoencephologram studies were normal on day 1. An echodense area in the subcortical white matter was seen by day 2. Other echodensities were detected by day 10. Computerized tomography studies showed areas of decreased attenuation in both hemispheres. Lung perfusion scan and renal-liver ultrasound studies were normal. All these cerebral and cardiac lesions were asymptomatic. Real-time ultrasonography is useful to diagnose asymptomatic endocardial thrombosis and its cerebral complications in premature infants.
Assuntos
Infarto Cerebral/etiologia , Cardiopatias/complicações , Doenças do Prematuro/diagnóstico por imagem , Trombose/complicações , Ecocardiografia Doppler , Feminino , Átrios do Coração , Cardiopatias/diagnóstico por imagem , Humanos , Recém-Nascido , Trombose/diagnóstico por imagemRESUMO
Ovarian fibromas in prepubertal girls are rare. We describe two girls aged 8 and 11 years with extensively calcified ovarian fibromas. One patient had a single unilateral fibroma with metaplastic bone formation in the calcified area. The other patient had bilateral nodular fibromas suggesting the possibility of naevoid basal-cell carcinoma syndrome although broader manifestations are lacking at present.
Assuntos
Calcinose/patologia , Fibroma/patologia , Neoplasias Ovarianas/patologia , Criança , Feminino , Humanos , PuberdadeRESUMO
A newborn male with Möbius syndrome, Poland anomaly, and dextrocardia is described. This is the second case reported of Poland-Möbius syndrome associated with dextrocardia. The patient presented with strabismus, facial diplegia, difficulty in swallowing, hypoplasia of the left pectoralis major muscle, partial absence of the upper costal cartilages, absence of the left areola, hypoplasia of the left forearm and hand, and dextrocardia without murmurs.