[Ehlers-Danlos syndrome associated with acute pancreatitis]. / Síndrome de Ehlers-Danlos asociado a pancreatitis aguda.

Ehlers-Danlos syndrome is an inherited connective tissue disease characterized by articular laxity, hyperelastic skin and tissue fragility. The syndrome is genetically, biochemically and clinically heterogeneous and several well-defined subtypes have been identified. We describe a patient with the type IV variant of this syndrome who developed acute spontaneous pancreatitis.