[Disorders of sino-atrial and auriculo-ventricular conduction in Steinert's disease. Apropos of one case]. / Troubles de la conduction sino-auriculaire et auriculo-ventriculaire dans la maladie de Steinert. A propos d'un cas

The authors report a case of Steinert's disease with disordered sino-atrial and atrio-ventricular conduction. The presence of sudden syncopal attacks and the absence of a cardiomyopathy (excluded by right- and leftsided haemodynamic studies and coronary arteriography) indicated the insertion of a definitive intra-cavitary pacemaker, especially as the life expectancy of this 54 year old patient did not seem to have been significantly reduced by his disease.