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1.
Rev. esp. patol ; 57(2): 128-132, Abr-Jun, 2024. ilus
Artigo em Inglês | IBECS | ID: ibc-232418

RESUMO

Primary hepatic liposarcoma is an extremely rare malignant tumour derived from adipocytes and is part of the group of mesenchymal tumours. We present the case of a 43-year-old Hispanic male patient with a pleomorphic hepatic liposarcoma and absence of MDM2 gene amplification. Two years and six months after surgery, the patient is asymptomatic. The present case is the first report of this entity with positive immunohistochemical testing for p16, p53, S100, vimentin and absence of MDM2 gene amplification. (AU)


El liposarcoma hepático primario es un tumor maligno extremadamente raro, derivado de adipocitos, y forma parte del grupo de tumores mesenquimales. Presentamos el caso de un paciente masculino de 43 años con diagnóstico de liposarcoma hepático pleomorfo con ausencia de amplificación del gen MDM2. Dos años y 6 meses después de la cirugía el paciente se encuentra asintomático. El presente caso es el primer informe de esta entidad con estudio inmunohistoquímico positivo para p16, p53, S100, vimentina y ausencia de amplificación del gen MDM2. (AU)


Assuntos
Humanos , Masculino , Adulto , Lipossarcoma , Neoplasias , Adipócitos , Células-Tronco Mesenquimais , Vimentina
2.
Rev Esp Patol ; 57(2): 128-132, 2024.
Artigo em Inglês | MEDLINE | ID: mdl-38599733

RESUMO

Primary hepatic liposarcoma is an extremely rare malignant tumour derived from adipocytes and is part of the group of mesenchymal tumours. We present the case of a 43-year-old Hispanic male patient with a pleomorphic hepatic liposarcoma and absence of MDM2 gene amplification. Two years and six months after surgery, the patient is asymptomatic. The present case is the first report of this entity with positive immunohistochemical testing for p16, p53, S100, vimentin and absence of MDM2 gene amplification.


Assuntos
Lipossarcoma , Proteínas Proto-Oncogênicas c-mdm2 , Humanos , Masculino , Adulto , Proteínas Proto-Oncogênicas c-mdm2/genética , Lipossarcoma/patologia , Adipócitos/patologia
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