RESUMO
Tumours of eccrine sweat glands are uncommon, with complex classification and different terms used even for the same tumour. Therefore, for practical purposes, it may be sufficient to differentiate between benign and malignant. Malignant eccrine hidradenoma has a predilection for head and neck, with high incidence of recurrence following surgical excision and also regional and distant metastases. We describe a case, which presented as a medical emergency with symptoms of severe anaemia and acute heart failure secondary to intermittent bleeding from a huge ulcerative neck lesion, which was subsequently diagnosed as eccrine hidradenocarcinoma. The tumour was successfully treated with complete surgical excision and reconstruction followed by radiotherapy. Two years postoperatively, the patient is very well with no sign of recurrence.
Assuntos
Acrospiroma/complicações , Adenoma de Glândula Sudorípara/complicações , Insuficiência Cardíaca/etiologia , Pescoço , Úlcera Cutânea/etiologia , Acrospiroma/fisiopatologia , Acrospiroma/terapia , Doença Aguda , Adenoma de Glândula Sudorípara/fisiopatologia , Adenoma de Glândula Sudorípara/terapia , Idoso , Anemia/etiologia , Emergências , Hemorragia/complicações , Hemorragia/etiologia , Humanos , Masculino , Úlcera Cutânea/complicações , Tomografia Computadorizada por Raios XRESUMO
O siringocistadenoma papilífero é um infreqüente hamartoma das glândulas sudoríparas, usualmente no couro cabeludo ou face. Observamos um siringocistadenoma papilífero do couro cabeludo em dois pacientes. O diagnóstico foi baseado no exame histológico. Exérese cirúrgica completa foi realizada. Alguns aspectos desta condição são discutidos
Assuntos
Humanos , Adenoma de Glândula Sudorípara/diagnóstico , Adenoma de Glândula Sudorípara/fisiopatologia , Adenoma de Glândula Sudorípara/terapiaRESUMO
BACKGROUND: The casual observation of a peritumoral edema with collagenolysis in a case of eccrine spiradenoma led us to search for similar lesions in a retrospective series of 50 spiradenomas. MATERIAL AND METHODS: Among 50 cases of eccrine spiradenomas, 36 excised with the overlying epidermis and the surrounding dermis were finally available for a conventional histologie study. RESULTS: In 14 cases, i.e. 39p. 100, we observed an edema above the tumour with thin and sparse collagen fibers and less altered elastic fibers. The clinical presentation of these 14 cases was not different from the general presentation of eccrine spiradenomas, but no precise photographical or clinical data were available. DISCUSSION: The cause of this epitumoral collagenolysis is unknown. It seems unrelated to the clear perivascular spaces often observed within the tumour lobules. It is of no help for diagnosis and may be considered as an unexplained curiosity like the elastolysis and the anetoderma seen above some pilomatricomas.
