Assuntos
Neoplasias Encefálicas/congênito , Neoplasias Encefálicas/patologia , Débito Cardíaco Elevado/congênito , Doenças Fetais/patologia , Teratoma/congênito , Teratoma/patologia , Neoplasias Encefálicas/diagnóstico , Débito Cardíaco Elevado/diagnóstico , Edema/congênito , Edema/diagnóstico , Feminino , Doenças Fetais/diagnóstico , Cabeça/anormalidades , Humanos , Crânio/patologia , Teratoma/diagnósticoRESUMO
Rapidly involuting congenital hemangioma (RICH) is a recently recognized entity in which the vascular tumor is fully developed at birth and undergoes rapid involution. Angiographic findings in two infants with congenital hemangioma are reported and compared with a more common postnatal infantile hemangioma and a congenital infantile fibrosarcoma. Congenital hemangiomas differed from infantile hemangiomas angiographically by inhomogeneous parenchymal staining, large and irregular feeding arteries in disorganized patterns, arterial aneurysms, direct arteriovenous shunts, and intravascular thrombi. Both infants had clinical evidence of a high-output cardiac failure and intralesional bleeding. This congenital high-flow vascular tumor is difficult to distinguish angiographically from arteriovenous malformation and congenital infantile fibrosarcoma.
Assuntos
Angiografia Digital , Neoplasias Encefálicas/congênito , Neoplasias Encefálicas/diagnóstico , Hemangioma/congênito , Hemangioma/diagnóstico , Débito Cardíaco Elevado/congênito , Débito Cardíaco Elevado/diagnóstico , Diagnóstico Diferencial , Feminino , Fibrossarcoma/congênito , Fibrossarcoma/diagnóstico , Humanos , Lactente , Bem-Estar do Lactente , Recém-Nascido , Imageamento por Ressonância Magnética , Masculino , Tomografia Computadorizada por Raios XRESUMO
A 45 year-old woman complaining of heart failure symptoms (New York Heart Association--class III) and a non typical thoracic pain was submitted to a transthoracic echocardiogram which showed a very dilated coronary artery and a fistula to the right atrium. The angiograms confirmed the same findings. She underwent open heart surgery which confirmed the diagnosis. Fistula ligation was then undertaken. She remains symptom-free three years after the operation.