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J Pediatr Surg ; 46(5): 817-22, 2011 May.
Artigo em Inglês | MEDLINE | ID: mdl-21616233

RESUMO

BACKGROUND/PURPOSE: For fetuses with giant neck masses and tracheal obstruction, an ex-utero intrapartum treatment (EXIT) procedure allows for safe nonemergent airway management while on placental support. Our objective was to examine fetal and maternal outcomes after EXIT procedure specifically for giant neck masses. METHODS: The medical records of all patients referred to a comprehensive fetal center for a giant neck mass between 2001 and 2010 were reviewed retrospectively. RESULTS: Among 24 patients referred, an EXIT procedure was performed in 12 with evidence of tracheal compression. An EXIT procedure was not performed because of minimal tracheal involvement (n = 8), elective abortion (n = 2), fetal demise (n = 1), or obstetric complication (n = 1). In all fetuses, the airway was successfully secured; tracheal intubation was achieved with rigid bronchoscopy (n = 10), direct laryngoscopy (n = 1), and tracheostomy (n = 1). Eleven patients survived to discharge, whereas 1 patient with significant pulmonary hypoplasia died 8 days after emergency EXIT procedure. Of 11 surviving infants, 10 are neurodevelopmentally intact. All mothers who desired future pregnancies have subsequently had uncomplicated deliveries (n = 6). CONCLUSIONS: Ex-utero intrapartum treatment procedure for giant neck mass can be performed safely for both mother and child. Most fetuses can be orotracheally intubated with minimal long-term morbidity. The potential for future pregnancies is preserved.


Assuntos
Manuseio das Vias Aéreas/métodos , Obstrução das Vias Respiratórias/terapia , Terapias Fetais/métodos , Neoplasias de Cabeça e Pescoço/cirurgia , Histerotomia/métodos , Intubação Intratraqueal/métodos , Linfangioma Cístico/cirurgia , Teratoma/cirurgia , Adulto , Obstrução das Vias Respiratórias/cirurgia , Anestesia por Inalação , Perda Sanguínea Cirúrgica , Broncoscopia , Cesárea , Tumor do Seio Endodérmico/congênito , Tumor do Seio Endodérmico/diagnóstico , Tumor do Seio Endodérmico/embriologia , Tumor do Seio Endodérmico/cirurgia , Feminino , Terapias Fetais/estatística & dados numéricos , Neoplasias de Cabeça e Pescoço/congênito , Neoplasias de Cabeça e Pescoço/diagnóstico , Neoplasias de Cabeça e Pescoço/embriologia , Hemangioendotelioma/congênito , Hemangioendotelioma/diagnóstico , Hemangioendotelioma/embriologia , Hemangioendotelioma/cirurgia , Hospitais Pediátricos/estatística & dados numéricos , Humanos , Recém-Nascido , Infertilidade Feminina/prevenção & controle , Intubação Intratraqueal/instrumentação , Linfangioma Cístico/diagnóstico , Linfangioma Cístico/embriologia , Complicações Pós-Operatórias/prevenção & controle , Gravidez , Diagnóstico Pré-Natal , Teratoma/congênito , Teratoma/diagnóstico , Teratoma/embriologia , Texas/epidemiologia , Traqueostomia , Resultado do Tratamento , Adulto Jovem
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