RESUMO
PURPOSE: To describe an unusual case of Müllerian agenesis associated with gonadal agenesis and thus sexual infantilism. MATERIALS AND METHODS: Pelvic magnetic resonance imaging (MRI) and sonography were performed and MRI of the kidneys. Pelvic sonography and serum follicle stimulating hormone (FSH) were also obtained. RESULTS: The only pelvic organ that this 15-year-old girl had was the distal portion of the vaginal canal. The kidneys were normal. CONCLUSIONS: This case suggests that at least in some cases some possible viral damaging process may lead to damage to both the ovaries and the Müllerian system. If there was a problem with the anti-Müllerian hormone (AMH), the kidney may be affected. Furthermore, AMH has nothing to do with the ovaries and a chance association of these two entities though possible, seems less likely than a common factor causing both problems.
