Assuntos
Miossarcoma/diagnóstico , Rabdomiossarcoma/diagnóstico , Neoplasias de Tecidos Moles/diagnóstico , Diagnóstico Diferencial , Genes p53/genética , Humanos , Miossarcoma/genética , Miossarcoma/cirurgia , Mutação Puntual/genética , Rabdomiossarcoma/genética , Rabdomiossarcoma/cirurgia , Neoplasias de Tecidos Moles/genética , Neoplasias de Tecidos Moles/cirurgiaRESUMO
PURPOSE: Retrorectal tumors are rare entities often found in females during reproductive age. Reports of retrorectal tumors complicating pregnancy are scant. This study presents two cases of retrorectal tumors complicating pregnancy and a literature review. METHODS: Two patients bearing retrorectal tumors diagnosed during pregnancy were referred to our care at the postpartum period. Both then underwent exploratory laparotomy. RESULTS: One patient had premature delivery by cesarean section because of hemorrhage from abruptio placentae followed by fetal mortality. Attempts to resect the tumor immediately after delivery had been unfruitful. The tumor was also unresectable on exploratory laparotomy. Biopsy studies of the tumor were consistent with low-grade myosarcoma. Another patient had a benign cystic mass that had been conservatively monitored throughout pregnancy. A healthy baby was delivered at term by cesarean section. The cyst was later resected via Kraske's incision and was diagnosed as cystic teratoma. CONCLUSIONS: Retrorectal tumors may cause significant local effects such as complicated pregnancy. Early detection in the population at risk is needed, as correct diagnosis and treatment may be done only on surgical exploration. During pregnancy, careful monitoring of advanced tumors is mandatory and may be sufficient to prevent maternal and fetal complications.
Assuntos
Miossarcoma/diagnóstico , Complicações Neoplásicas na Gravidez/diagnóstico , Neoplasias Retais/diagnóstico , Neoplasias Retroperitoneais/diagnóstico , Teratoma/diagnóstico , Adulto , Cesárea , Feminino , Humanos , Miossarcoma/cirurgia , Trabalho de Parto Prematuro/etiologia , Gravidez , Complicações Neoplásicas na Gravidez/cirurgia , Neoplasias Retais/cirurgia , Neoplasias Retroperitoneais/cirurgia , Teratoma/cirurgiaRESUMO
O Liomiossarcoma de Esofago e uma neoplasia rara, com 45 casos descritos na literatura inglesa ate 1986. E descrito um caso e feita breve revisao bibliografica. A molestia acomete ambos os sexos em igual proporcao. Os achados clinicos e radiologicos simulam outras doencas do mediastino ou do esofago. O tratamento de escolha e a cirurgia. Pacientes do sexo feminino e portadores de lesao polipoide parecem ter melhor prognostico