A rare case of congenital ranula.

Simple ranula is a cystic swelling confined to the floor of mouth while plunging ranula presents with extension to the neck. Congenital ranula presenting with symptoms of feeding difficulties is a very rare occurrence. There is paucity of literature regarding the management of large congenital ranula. Varied treatment options are described for the management of ranula with variable recurrence rate. In paediatric and adult patients, ranula is considered as a type of extravasation cyst and removal of sublingual gland is advocated to remove the sources of extravasation. Congenital ranula is usually a variant of retention cyst and should be treated with marsupialisation or simple excision of cyst while cyst excision with sublingual sialadenectomy should be reserved for recurrent cases.

Prenatal Diagnosis and Intrapartum Management of Congenital Ranula.

A foetal sublingual cystic lesion was diagnosed by routine prenatal ultrasonography at 27 weeks of gestation. Foetal growth and amniotic fluid volume were normal. An ex utero intrapartum treatment (EXIT) procedure was performed, and the cyst was aspirated to allow breathing during planned Caesarean section. The cyst was totally excised when the newborn was 60 days old, and histopathological examination revealed a mucous cyst of the mouth floor.

Congenital Ranula: A Case Report and Literature Review.

Ranula consists of a pathological process induced by ductal disruption of the minor salivary glands followed by extravasation of mucous material surrounding adjacent structures. A swelling causing breathing and feeding problems associated with tongue displacement is frequently observed. It is a disease that generally involves the younger age group. In newborns congenital ranula may occur, an uncommon variance that differs from common ranula by not relate to post-traumatic reactions. There are reports that indicate a salivary gland duct atresia as the main cause of this pathology. The aim of this study is to analyze the clinicopathological characteristics of congenital ranula by reporting a new case report of this salivary cyst and reviewing the case reports previously published in the English literature.

A case of imperforate Wharton duct.

Congenital oral masses are rare entities. The establishment of formal fetal diagnostic teams has led to an increased antenatal detection of such lesions. The congenital ranula is a distinct entity from the more familiar variant presenting later in life. The congenital variant may result from an anomaly of the Wharton duct with subsequent dilation of the duct. The variant presenting later in life is the more familiar mucous extravasation phenomenon in the floor of the mouth. Management of the congenital ranula is distinct from its noncongenital counterpart and more conservative and is discussed in the present report.

Rânula congênita: diagnóstico ultrassonográfico antenatal / Congenital ranula: antenatal sonographic diagnosis

Rânula congênita uma rara malformação cística visualizada na cavidade oral. É um pseudocisto habitualmente localizado no espaço sublingual entre o músculo milo-hioideo e a mucosa da língua. Relata-se um caso de gestante de 24 anos, G3P2, com idade gestacional de 29 semanas, encaminhada por conta de polidrâmnio e grande massa de cavidade oral de natureza cística.

A congenital ranula is a rare cystic malformation seen in the oral cavity. This pseudocyst is normally located in the sublingual space between the mylohyoid muscle and the lingual mucosa. A 24-year-old woman, gravida 3, para 2, at 29 weeks' gestation was referred to our institution because of polihydramnios and large oral mass.

[Congenital ranula]. / Rânula congénita.

The authors describe a case of congenital ranula diagnosed by a routine prenatal ultrasonography at 21 weeks of gestation. The fetal kariotype was normal. Follow-up ultrasound scans revealed no changes in the size or the position of the cyst. Fetal growth was normal as was the amniotic fluid volume. Surgical treatment was performed 3 days after a normal vaginal delivery, with excellent results.

Congenital ranula.

This article presents 3 cases of infants with congenital ranula, a rare salivary gland pathology. Pathophysiology is discussed, differential diagnosis, and different treatment choices are explained.

Plunging ranula: congenital or acquired?

OBJECTIVE: To review our clinical experience with plunging ranula and examine the evidence in support of our impression that plunging ranula has a genetic basis. STUDY DESIGN: Case series with chart review. SETTING: Secondary otolaryngology service. SUBJECTS AND METHODS: Review of the medical records of a clinical series of 80 consecutive plunging ranulas in 77 patients was conducted, with recording of clinical and radiological findings, surgical treatment, and outcome. A literature review using MEDLINE and OLD MEDLINE was performed. RESULTS: The majority of plunging ranulas had no intraoral component on clinical examination, although evidence of mucus extravasation from the sublingual gland could be found both radiologically and histologically in all cases. There were four patients with bilateral plunging ranula and one instance of siblings with unilateral plunging ranula. Maoris and Polynesians comprised more than 82 percent of our cases; this was a significant overrepresentation of these ethnic groups (P < 0.0001). A very strong predominance of cases of Chinese origin was also evident in the literature. CONCLUSION: The clinical findings and the supporting data from the literature, when viewed in light of information relating to the known anatomical anomaly of a dehiscence in the mylohyoid muscle and ectopic sublingual gland lying below the plane of the mylohyoid, appear to support the case for a genetic basis for this unusual clinical entity.

Prenatal ultrasound and magnetic resonance imaging depiction of a small sublingual ranula.

Prenatal diagnosis of a congenital ranula has rarely been reported. We describe the case of a small ranula depicted on prenatal sonogram and magnetic resonance imaging, in which we could confirm the intact airway. Although the size of the ranula noted in our fetus was the smallest among the cases reported in the English literature, both of these imaging modalities clearly presented typical diagnostic features present on both ultrasound and magnetic resonance imaging.

Congenital ranula: a case report.

The purpose of this study was to report a case of bilateral swelling on the floor of the mouth of a 7-month-old patient. The lesion was congenital and had started to cause feeding problems. After the clinical diagnosis of ranula was made, the lesion was marsupialized. The obtained specimen was submitted for histopathological examination, which revealed an epithelial-lined cystic lesion. These results led to the final diagnosis of mucus retention cyst. After an 8-year follow-up period, the patient is in good general health with no recurrences.

Congenital neck masses.

Congenital neck lesions reflect abnormal embryogenesis in head and neck development. A thorough knowledge of embryology and anatomy is critical in the diagnosis and treatment of these lesions. The appropriate diagnosis of these lesions is necessary to provide appropriate treatment and long-term follow up, because some of these lesions may undergo malignant transformation or be harbingers of malignant disease.

[Congenital ranula in a newborn]. / Sublinguale, livide Schwellung am Mundboden eines Neugeborenen: Kongenitale Ranula.

Ranulas are cystic lesions in the floor of the mouth. They are either retention cysts of the excretory duct of the sublingual gland or pseudocysts formed by excretory duct rupture followed by extravasation and accumulation of mucus in the surrounding tissue. We report the case of a premature newborn with a congenital ranula in the floor of mouth. The ranula caused no discomfort or complications, so that immediate intervention was not necessary. The cyst resolved completely by the age of 4 months. Complications in newborns especially include airway obstruction and feeding difficulties. Surgical treatment options are needle aspiration, excision of the ranula, marsupialization, cryosurgery, and--in addition to excision of the cyst--removal of the ipsilateral sublingual gland. Sclerotherapy has shown good results as well. As many congenital cysts resolve or rupture spontaneously, they should be observed for potential resolution for several months in uncomplicated cases.

Ex utero intrapartum treatment (EXIT) for congenital giant ranula.

UNLABELLED: Congenital giant ranula causing life-threatening upper airway obstruction is a rare condition. A well-planned ex utero intrapartum treatment (EXIT) procedure for aspiration and decompression of the cystic lesion is simple, efficacious and effective in securing a patent airway before the fetus is completely delivered, and may prevent lifelong neurodevelopmental complications associated with perinatal asphyxia in such cases. CONCLUSION: EXIT could be a life-saving procedure for congenital giant ranula.

[Diagnostic image (229). A neonate with a sublingual swelling]. / Diagnose in beeld (229). Een neonatus met een sublinguale zwelling.

A male neonate presented with a right-sided swelling in the floor of the mouth, a congenital ranula, which disappeared spontaneously.

Prenatal diagnosis of ranula at 21 weeks of gestation.

A fetal sublingual cystic lesion was diagnosed by routine prenatal ultrasonography at 21 weeks of gestation and followed up until term in a tertiary care center. Fetal growth was normal as was the amniotic fluid volume. Ex utero intrapartum treatment was performed and the cyst was aspirated to allow breathing and swallowing during planned Cesarean section. The cyst was totally excised when the newborn was 27 days of age and histological examination revealed a mucous cyst of the mouth floor.

Congenital ranula. A report of two cases.

We report 2 unusual cases of congenital ranula in male Nigerian infants. Clinical examination could not discern the orifice of the submandibular duct on the affected sides, while a lower occlusal radiograph revealed no obvious calculi. Diagnosis was mainly by clinical presentation. The paper highlights possible aetiopathogenesis, clinical aspects and diagnostic features. Emphasis is laid on the need for careful evaluation of oral ranulas in order to discern their origin and provide appropriate treatment.

Recurrent congenital bilateral ranula: a case report.

A case of congenital bilateral ranula in a one-week-old male baby is reported. At presentation the cyst measured 3.5 x 2.5 cm but did not interfere with feeding. Initial marsupialisation resulted in recurrence of the cyst. It was subsequently re-excised completely together with the associated sublingual salivary gland. The cyst has not recurred six months after treatment. The usually large size of the cyst and its bilateral presentation makes this an interesting case.