Ectasia congénita de las arterias coronarias e hiperinsulinismo: ¿sólo una coincidencia? / Congenital ectasia of coronary e hyperinsulinism: just a coincidence?

Se presenta el caso de un recién nacido con ectasia congénita de las arterias coronarias. Se repasan la frecuencia, la etiología, la clínica y la evolución de esta entidad, así como su posible relación con el hiperinsulinismo que también presentaba el paciente (AU)

The case of a newborn with congenital coronary artery ectasia is presented. Frequency, etiology, and clinical evolution of this entity and its possible relationship with hyperinsulinism also presented the patient is reviewed (AU)

Congenital coronary artery obstruction associated with aortic anomalies in children: report of two cases.

Coronary arterial obstruction associated with congenital aortic valve disease is rare in children. We studied two children with aortic valve disease and symptoms of coronary insufficiency. Cineangiography revealed localized obstruction of the proximal left coronary artery. In one patient, a membrane-like structure partially covered the left sinus of Valsalva, almost isolating the ostium of the left coronary artery; the other patient had severe stenosis of the proximal left coronary artery and a congenitally hypoplastic left coronary cusp. Surgical repair was successful in both cases. Symptoms of myocardial ischemia in children with aortic valve disease should be investigated promptly to exclude obstruction of the coronary arteries.