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Tumor maligno congénito. Síndrome de Pepper / Congenital malignant tumor: Pepper's Syndrome
Casale, Roberto; Pascale, Julián; Sar, Juan Sebastián; González, Mariela C; Rodríguez, Carolina.
Affiliation
  • Casale, Roberto; Hospital Nacional Prof. Alejandro Posadas. Departamento Materno Infantil. Buenos Aires. AR
  • Pascale, Julián; Hospital Nacional Prof. Alejandro Posadas. Servicio de Obstetricia. Buenos Aires. AR
  • Sar, Juan Sebastián; Hospital Nacional Prof. Alejandro Posadas. Servicio de Obstetricia. Buenos Aires. AR
  • González, Mariela C; Hospital Interzonal General de Agudos "Prof. Dr. Luis Güemes". Buenos Aires. AR
  • Rodríguez, Carolina; Hospital Nacional Prof. Alejandro Posadas. Buenos Aires. AR
Prensa méd. argent ; 104(4): 190-195, Jun2018. fig
Article in Spanish | BINACIS, LILACS | ID: biblio-1051980
Responsible library: AR392.1
ABSTRACT
Pepper's syndrome refers to a neuroblastoma originated in the adrenal glands that usually metastasizes to the liver with abdominal development and respiratory involvement because of thoracic compression. The metastasic tumors are usually infrequent with an unfavorable prognosis. The cases reported in the world literature are very few. The congenital form of neuroblastoma is uncommon. The aim of this report was to describe a typical clinical case of a new born who died because of a metastasic malignant tumor, comptible with a Pepper's syndrome
Subject(s)
Collection: International databases Database: BINACIS / LILACS Main subject: Autopsy / Hydrops Fetalis / Adrenal Gland Neoplasms / Stillbirth / Hepatomegaly / Neoplasm Metastasis / Neuroblastoma Type of study: Prognostic study Limits: Female / Humans / Infant, Newborn Language: Spanish Journal: Prensa méd. argent Journal subject: Medicine Year: 2018 Document type: Article Affiliation country: Argentina Institution/Affiliation country: Hospital Interzonal General de Agudos "Prof. Dr. Luis Güemes"/AR / Hospital Nacional Prof. Alejandro Posadas/AR
Collection: International databases Database: BINACIS / LILACS Main subject: Autopsy / Hydrops Fetalis / Adrenal Gland Neoplasms / Stillbirth / Hepatomegaly / Neoplasm Metastasis / Neuroblastoma Type of study: Prognostic study Limits: Female / Humans / Infant, Newborn Language: Spanish Journal: Prensa méd. argent Journal subject: Medicine Year: 2018 Document type: Article Affiliation country: Argentina Institution/Affiliation country: Hospital Interzonal General de Agudos "Prof. Dr. Luis Güemes"/AR / Hospital Nacional Prof. Alejandro Posadas/AR
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