Melkersson-rosenthal: reporte de caso clínico de una neurodermatosis infrecuente / Melkersson-rosenthal syndrome: case report of an uncommon neurodermatosis
Rev. argent. dermatol
; 101(1): 71-80, mar. 2020. graf
Article
in Spanish
| LILACS
| ID: biblio-1125808
Responsible library:
AR635.1
RESUMEN
Resumen El síndrome de Melkersson-Rosenthal (SMR) es una entidad clínica rara, de patogénesis desconocida. Se manifiesta característicamente por edema orofacial recidivante, lengua fisurada y parálisis recurrente del nervio facial. Representando así undesafío diagnóstico y terapéutico, además de generar importante compromiso social al individuo acometido. El presente artículo tiene como objetivo describir el caso de un paciente de 15años de edad que presentó edema labial, lengua fisurada y queilitis granulomatosa al examen histopatológico, llevándose a consideración la hipótesis del síndrome citado, con resultados satisfactorios al tratamiento establecido.
ABSTRACT
Abstract Melkersson-Rosenthal syndrome (MRS) is a rare clinical entity with an unknown pathogenesis. It clinically manifests in orofacial edema, plicated tongue and recurrent paralysis of the facial nerve. It represents a diagnostic and therapeutic challenge, and has an important psycosocial impact on the affected individual. This study describes the case of a 15-year-old patient who presented with labial edema, plicated tongue and granulomatous cheilitis on histopathological examination, for which a diagnosis of MRS was proposed. The patient showed a good response to treatment.
Full text:
Available
Collection:
International databases
Database:
LILACS
Main subject:
Tongue, Fissured
/
Edema
/
Facial Nerve
/
Melkersson-Rosenthal Syndrome
Type of study:
Diagnostic study
/
Etiology study
Limits:
Adolescent
/
Humans
/
Male
Language:
Spanish
Journal:
Rev. argent. dermatol
Journal subject:
Dermatology
Year:
2020
Document type:
Article
Affiliation country:
Brazil
/
Colombia
Institution/Affiliation country:
Universidad Federal de São João del-Rei/BR
/
Universidad Libre Seccional Barranquilla/CO