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Systemic sarcoidosis presenting as acute rapidly progressive proptosis / Sarcoidose sistêmica apresentando-se como proptose aguda rapidamente progressiva
Silva, Maria Valeria da; Chavez, Yael; Nicola, Maria Laura Di; Delabie, Jan M. A.; Rose, Kalpana; Krema, Hatem.
Affiliation
  • Silva, Maria Valeria da; Princess Margaret Cancer Centre. Toronto. CA
  • Chavez, Yael; Princess Margaret Cancer Centre. Toronto. CA
  • Nicola, Maria Laura Di; Princess Margaret Cancer Centre. Toronto. CA
  • Delabie, Jan M. A.; University of Toronto. University Health Network. Department of Pathology. Toronto. CA
  • Rose, Kalpana; Princess Margaret Cancer Centre. Toronto. CA
  • Krema, Hatem; Princess Margaret Cancer Centre. Toronto. CA
Arq. bras. oftalmol ; 86(2): 168-170, Mar.-Apr. 2023. graf
Article in English | LILACS-Express | LILACS | ID: biblio-1429839
Responsible library: BR1.1
ABSTRACT
ABSTRACT Sarcoidosis is a generalized systemic chronic inflammation that rarely involves the orbit. As a chronic inflammation, sarcoidosis typically manifests with an insidious onset and slowly progressive course. We report a case of acute-onset proptosis resulting from a rapidly growing diffuse orbital mass that simulated malignant growth, which was biopsy proven to be the first manifestation of systemic sarcoidosis. The patient demonstrated complete resolution of proptosis and systemic involvement with long-term corticosteroid treatment.
RESUMO
RESUMO A sarcoidose é uma inflamação sistêmica generalizada que raramente envolve a órbita. Sendo uma inflamação crônica, a sarcoidose geralmente se manifesta com um início insidioso e uma evolução lentamente progressiva. Neste artigo, é relatado um caso de proptose de início agudo, resultante de uma massa orbitária difusa de rápido crescimento, simulando um crescimento maligno, mas cuja biópsia comprovou ser a primeira manifestação de uma sarcoidose sistêmica. O paciente apresentou resolução completa da proptose e do envolvimento sistêmico com tratamento de longo prazo com corticosteroides.


Full text: Available Collection: International databases Database: LILACS Language: English Journal: Arq. bras. oftalmol Journal subject: Ophthalmology Year: 2023 Document type: Article Affiliation country: Canada Institution/Affiliation country: Princess Margaret Cancer Centre/CA / University of Toronto/CA

Full text: Available Collection: International databases Database: LILACS Language: English Journal: Arq. bras. oftalmol Journal subject: Ophthalmology Year: 2023 Document type: Article Affiliation country: Canada Institution/Affiliation country: Princess Margaret Cancer Centre/CA / University of Toronto/CA
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