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Fibrosis endomiocárdica / Endomyocardial fibrosis
Rodríguez-González, María Juliana; Torres, Ángela M; Echeverría, Luis E.
Affiliation
  • Rodríguez-González, María Juliana; Fundación Cardiovascular de Colombia. Floridablanca. CO
  • Torres, Ángela M; Fundación Cardiovascular de Colombia. Floridablanca. CO
  • Echeverría, Luis E; Fundación Cardiovascular de Colombia. Floridablanca. CO
Rev. colomb. cardiol ; 24(4): 407-407, jul.-ago. 2017. tab, graf
Article in Spanish | LILACS, COLNAL | ID: biblio-900552
Responsible library: CO369.9
RESUMEN
Resumen Las miocardiopatías son trastornos intrínsecos del músculo cardíaco. Presentan fenotipos diferenciales que determinan su clasificación; estos son dilatada, hipertrófica, restrictiva, displasia arritmogénica del ventrículo derecho y no clasificadas. Las miocardiopatías restrictivas se caracterizan por ventrículos de tamaño normal, con grosores de pared normales o ligeramente aumentados, paredes rígidas, disfunción diastólica severa y llenado restrictivo con presiones elevadas. Una de las formas más comunes de miocardiopatía restrictiva es la fibrosis endomiocárdica la cual es endémica en algunas zonas tropicales especialmente en África (países de bajos ingresos), pero en nuestro medio hay pocos reportes de aparición. Su etiología es desconocida, aunque existen diversos mecanismos que han sido involucrados en su fisiopatología. Su diagnóstico se basa en estudios imagenológicos (ecocardiograma transtorácico y resonancia magnética nuclear cardíaca). El pronóstico es muy pobre, y usualmente se diagnostica en etapas muy avanzadas de la enfermedad. Se describe el caso de una paciente femenina, adulta media, que debutó con cardiopatía restrictiva, cuyo diagnóstico final fue fibrosis endomiocárdica.
ABSTRACT
Abstract Cardiomyopathies are intrinsic conditions of the cardiac muscle. They present differential phenotypes that determine their classification. These are dilated, hypertrophic, restrictive, arrhythmogenic right ventricular and unclassified. Restrictive cardiomyopathies are characterised by larger than normal ventricles with normal or slightly enlarged thickness of the walls, rigid walls, severe diastolic dysfunction and restrictive filling with high pressures. One of the most common restrictive cardiomyopathies is endomyocardial fibrosis, which is endemic to some tropical areas, especially Africa (low income countries), but there are few reports of its occurrence in our environment. Its aetiology is unknown, but there are several mechanisms that have been involved in its pathophysiology. Its diagnosis is based in imaging studies (transthoracic echocardiogram, cardiac nuclear magnetic resonance). Prognosis is very poor, and it is usually diagnoses in the latest stages of the disease. The case of a female, average adult patient that debuted with restrictive cardiomyopathy with a final diagnosis of endomyocardial fibrosis is described.
Subject(s)


Full text: Available Collection: International databases Database: COLNAL / LILACS Main subject: Cardiomyopathy, Restrictive / Endomyocardial Fibrosis Type of study: Prognostic study Limits: Female / Humans Language: Spanish Journal: Rev. colomb. cardiol Journal subject: Cardiology Year: 2017 Document type: Article Affiliation country: Colombia Institution/Affiliation country: Fundación Cardiovascular de Colombia/CO

Full text: Available Collection: International databases Database: COLNAL / LILACS Main subject: Cardiomyopathy, Restrictive / Endomyocardial Fibrosis Type of study: Prognostic study Limits: Female / Humans Language: Spanish Journal: Rev. colomb. cardiol Journal subject: Cardiology Year: 2017 Document type: Article Affiliation country: Colombia Institution/Affiliation country: Fundación Cardiovascular de Colombia/CO
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