Síndrome de Sneddon asociado a síndrome antifosfolipídico: descripciones clínicas y revisión de la literatura / Sneddon syndrome associated with antiphospholipid syndrome: clinical descriptions and a literature review
Rev. colomb. reumatol
; 24(3): 185-188, jul.-set. 2017. graf
Article
in Es
| LILACS
| ID: biblio-900874
Responsible library:
CO356.9
RESUMEN
Resumen El síndrome de Sneddon es una rara vasculopatía no inflamatoria, obliterante, caracterizada por la asociación de eventos cardiovasculares (hipertensión arterial, claudicación intermitente y enfermedad coronaria), neurológicas (accidentes cerebrovasculares isquémicos, cefalea, vértigo y convulsiones) y livedo reticularis de tipo racemosa. Presentamos a una mujer que ingresa con un cuadro neurológico isquémico, hipertensión arterial, problemas vasculares y lesiones en piel. La biopsia de piel se catalogó como dermatitis perivascular superficial linfocitaria, sugestivo de lesión oclusiva.
ABSTRACT
Abstract Sneddon syndrome is a rare non-inflammatory obliterative vasculopathy, characterised by the association of cardiovascular (arterial hypertension, intermittent claudication, and coronary artery disease) and neurological events (ischaemic stroke, headache, dizziness and convulsions), and livedo reticularis/livedo racemosa. The case is presented of a woman admitted with an ischaemic neurological disease, hypertension, vascular problems, and skin lesions. The skin biopsy was classified as surface perivascular lymphocytic dermatitis, suggestive of occlusive lesion.
Key words
Full text:
1
Collection:
01-internacional
Database:
LILACS
Main subject:
Antiphospholipid Syndrome
/
Sneddon Syndrome
Type of study:
Risk_factors_studies
/
Systematic_reviews
Limits:
Adult
/
Female
/
Humans
Language:
Es
Journal:
Rev. colomb. reumatol
Journal subject:
REUMATOLOGIA
Year:
2017
Document type:
Article
Affiliation country:
Peru
Country of publication:
Colombia