Cianosis en un paciente de 14 años: Presentación de un caso de metahemoglobinemia / Cyanosis in 14-year-old patient: Methemoglobinemia: case report
Arch. argent. pediatr
; 116(3): 429-432, jun. 2018. tab, ilus
Article
in Spanish
| LILACS, BINACIS
| ID: biblio-950020
Responsible library:
AR94.1
RESUMEN
La cianosis es la coloración azulada de la piel y las mucosas debida al aumento de la concentración de hemoglobina reducida en los capilares o a la presencia de metahemoglobina en concentraciones mayores de las normales. Es importante pensar en metahemoglobinemia como diagnóstico diferencial frente a un paciente con cianosis que no responde a la administración de oxígeno cuando no existen causas cardiorrespiratorias que la justifiquen, dado que requiere de otros métodos diagnósticos y de tratamiento específico. Se presenta el caso de un paciente adolescente de 14 años de edad con cianosis secundaria a metahemoglobinemia de probable etiología congénita. Se discuten las causas, forma de presentación, diagnóstico y tratamiento.
ABSTRACT
The bluish coloration of skin and mucous membranes, called as cyanosis, could be explained by high reduced hemoglobin in the capillaries, or the presence of elevated methemoglobin concentration. It is important to think of methemoglobinemia as a differential diagnosis in a cyanotic patient who does not respond to oxygen administration once cardiorespiratory causes are discarded; since it requires other diagnostic methods and specific treatment. We described a case of cyanosis in a fourteen-year-old adolescent with probable congenital methemoglobinemia. We discussed their probable causes, clinic presentation, diagnosis and treatment.
Full text:
Available
Collection:
International databases
Database:
BINACIS
/
LILACS
Main subject:
Cyanosis
/
Methemoglobinemia
Type of study:
Diagnostic study
Limits:
Adolescent
/
Humans
/
Male
Language:
Spanish
Journal:
Arch. argent. pediatr
Journal subject:
Pediatrics
Year:
2018
Document type:
Article
Affiliation country:
Argentina
Institution/Affiliation country:
Hospital de Niños Superiora Sor María Ludovica/AR