Enfermedad de Hailey-Hailey en varias generaciones de una familia / Hailey - Hailey disease in several generations of a family
Medisan
; 16(12)sept. 2012. ilus
Article
in Spanish
| CUMED
| ID: cum-52959
Responsible library:
CU418.1
RESUMEN
Se describen 2 casos clínicos de hermanos adultos que presentaban pénfigo benigno familiar o enfermedad de Hailey-Hailey, tipo de genodermatosis por alteración en la cohesión epidérmica, atendidos en el Hospital General Docente Dr Juan Bruno Zayas Alfonso de Santiago de Cuba. Los pacientes fueron tratados con esteroides en dosis antiinflamatorias, antibióticos y, de forma tópica, linimento vegetal y crema de aloe, además de recibir terapia floral. De manera general, ambos mejoraron su cuadro clínico durante la estadía en dicha institución hospitalaria(AU)
ABSTRACT
Two case reports of adult siblings are described, who presented with benign familial pemphigus or Hailey-Hailey disease --type of genodermatosis by altered epidermal cohesion-- attended in Dr Juan Bruno Zayas Alfonso Teaching General Hospital of Santiago de Cuba. Patients were treated with steroids at anti-inflammatory doses, antibiotics, and topical plant liniment and aloe cream, besides receiving flower therapy. In general, both of them improved the clinical picture during their stay in this institution(AU)
Full text:
Available
Collection:
National databases
/
Cuba
Database:
CUMED
Main subject:
Steroids
/
Pemphigus, Benign Familial
/
Anti-Bacterial Agents
Limits:
Adult
/
Humans
/
Male
Language:
Spanish
Journal:
Medisan
Year:
2012
Document type:
Article
Institution/Affiliation country:
Hospital General Docente Dr Juan Bruno Zayas/Cuba
/
Policlínico Comunitario América 1/Cuba