Reticulohistiocitosis cutánea difusa / Diffuse cutaneous reticulohistiocytosis
Actas dermo-sifiliogr. (Ed. impr.)
; 97(2): 118-121, mar. 2006. ilus
Article
in Es
| IBECS
| ID: ibc-043558
Responsible library:
ES1.1
Localization: ES1.1 - BNCS
RESUMEN
Las reticulohistiocitosis constituyen un grupo heterogéneo de enfermedades que tienen su origen en la acumulación de células de estirpe histiocitaria en diferentes tejidos y fundamentalmente en la piel. Se han descrito tres formas clínicas principales (multicéntrica, solitaria, cutánea difusa) que presentan idénticas características histológicas, ultraestructurales e inmunohistoquímicas. Presentamos un caso de reticulohistiocitosis cutánea difusa que constituye el patrón clínico menos común dentro del espectro de esta enfermedad
ABSTRACT
The reticulohistiocytoses make up a heterogeneous group of diseases whose origin lies in an accumulation of cells of histiocytic lineage in different tissues and primarily in the skin. Three main clinical forms have been described (multicentric, solitary, diffuse cutaneous), which present with identical histological, ultrastructural and immunohistochemical characteristics. We present a case of diffuse cutaneous reticulohistiocytosis, which is the least common clinical pattern in the spectrum of this disease
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Collection:
National databases
/
Spain
Database:
IBECS
Main subject:
Biopsy
/
Immunohistochemistry
/
Tomography, Emission-Computed
/
Histiocytosis
Type of study:
Diagnostic study
Limits:
Humans
/
Male
Language:
Spanish
Journal:
Actas dermo-sifiliogr. (Ed. impr.)
Year:
2006
Document type:
Article
Institution/Affiliation country:
Hospital Universitario Reina Sofía/España