Adenocarcinoma gástrico en el síndrome de Zinsser-Cole-Engman / Gastric adenocarcinoma in Zinsser-Cole-Engman syndrome
Cir. Esp. (Ed. impr.)
; 80(3): 176-177, sept. 2006. tab
Article
in Es
| IBECS
| ID: ibc-048135
Responsible library:
ES1.1
Localization: ES1.1 - BNCS
RESUMEN
El síndrome de Zinsser-Cole-Engman es una disqueratosis congénita que causa alteraciones cutáneas, hematológicas y, en un 5% de los casos, neoplasias digestivas. Presentamos el caso de un varón de 37 años afectado de este síndrome en cuya evolución se diagnosticó un adenocarcinoma gástrico. Este caso es un ejemplo de cómo se debería manejar a estos pacientes para identificar neoplasias en estadios en los que el tratamiento es curativo (AU)
ABSTRACT
Zinsser-Cole-Engman syndrome is a congenital dyskeratosis that produces cutaneus and hematologic alterations and, in 5% of patients, gastrointestinal neoplasms. We report the case of a 37-year-old man with this syndrome who was diagnosed with gastric adenocarcinoma. This case provides an example of the management that should be followed with these patients in order to identify neoplasms at stages in which treatment is curative (AU)
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Collection:
National databases
/
Spain
Database:
IBECS
Main subject:
Stomach Neoplasms
/
Dyskeratosis Congenita
Type of study:
Prognostic study
Limits:
Adult
/
Humans
/
Male
Language:
Spanish
Journal:
Cir. Esp. (Ed. impr.)
Year:
2006
Document type:
Article
Institution/Affiliation country:
Consorcio Hospital General Universitario de Valencia/España