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Seudohermafroditismo masculino / Male pseudohermaphroditism
Tapia Ceballos, L; López Siguero, J. P; Río Camacho, G. del; Audí Parera, L; Martín Torrecillas, A; Martínez Aedo, M. J.
Affiliation
  • Tapia Ceballos, L; Hospital Costa del Sol. Marbella. España
  • López Siguero, J. P; Hospital Carlos Haya. Málaga. España
  • Río Camacho, G. del; Hospital Costa del Sol. Marbella. España
  • Audí Parera, L; Hospital Materno-Infantil Vall d'Hebron. Barcelona. España
  • Martín Torrecillas, A; Hospital Costa del Sol. Marbella. España
  • Martínez Aedo, M. J; Hospital Carlos Haya. Málaga. España
An. pediatr. (2003, Ed. impr.) ; 67(1): 57-60, jul. 2007. ilus
Article in Es | IBECS | ID: ibc-055328
Responsible library: ES1.1
Localization: ES1.1 - BNCS
RESUMEN
El abordaje de un recién nacido (RN) con genitales ambiguos es una urgencia de difícil manejo, no sólo urge el diagnóstico de entidades que podrían implicar una pérdida salina, sino también la asignación del sexo al RN antes de que éste fije su sexo psicológico. Presentamos 2 casos de seudohermafroditismo masculino, uno de ellos del tipo hermafroditismo verdadero y el otro secundario a un déficit de 5alfa-reductasa. Se analiza la fisiología de la diferenciación sexual, las entidades diagnósticas y el protocolo que hay que seguir
ABSTRACT
Diagnosis of ambiguous genitalia in a newborn is an emergency that can be difficult to manage, not only because salt wasting entities must be ruled out, but also due to the importance of gender assignment before psychological gender is established. We report two cases of male pseudohermaphroditism, a true hermaphroditism and a 5-alfa-reductase deficiency. The physiology of sexual differentiation and diagnosis, as well as the management of these infants, are discussed
Subject(s)
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Collection: National databases / Spain Database: IBECS Main subject: Sex Differentiation / Disorders of Sex Development Type of study: Diagnostic study / Etiology study / Practice guideline Limits: Humans / Male / Infant, Newborn Language: Spanish Journal: An. pediatr. (2003, Ed. impr.) Year: 2007 Document type: Article Institution/Affiliation country: Hospital Carlos Haya/España / Hospital Costa del Sol/España / Hospital Materno-Infantil Vall d'Hebron/España
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Collection: National databases / Spain Database: IBECS Main subject: Sex Differentiation / Disorders of Sex Development Type of study: Diagnostic study / Etiology study / Practice guideline Limits: Humans / Male / Infant, Newborn Language: Spanish Journal: An. pediatr. (2003, Ed. impr.) Year: 2007 Document type: Article Institution/Affiliation country: Hospital Carlos Haya/España / Hospital Costa del Sol/España / Hospital Materno-Infantil Vall d'Hebron/España
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