Fibrodisplasia osificante progresiva. El papel del cirujano oral y maxilofacial. Experiencia en 2 casos / Fibrodysplasia ossificans progressiva. The role of oral and maxillofacial surgeon. experience in two cases
Rev. esp. cir. oral maxilofac
; 36(2): 73-77, abr.-jun. 2014. ilus
Article
in Spanish
| IBECS
| ID: ibc-122807
Responsible library:
ES1.1
Localization: BNCS
RESUMEN
La fibrodisplasia osificante progresiva es un raro desorden genético que se caracteriza por la asociación de malformaciones congénitas y brotes de osificación heterotópica progresiva desde los primeros an os de vida.El escaso número de pacientes que padecen la enfermedad, hace que el curso y tratamiento de la misma sea desconocida para muchos especialistas, pese a la importancia del manejo multidisciplinar de estos pacientes. Se presentan 2 casos valorados por nuestro servicio en los últimos 12 meses; 2 varones de 40 y 23 an os diagnosticados de fibrodisplasia osificante progresiva en la infancia que acudieron a la consulta de cirugía maxilofacial para valoración y tratamiento (AU)
ABSTRACT
The ossificans progressive fibrodysplasia is a rare genetic disorder that is characterized by the association of congenital malformations and progressive heterotopic ossification outbreaks since the early years of life. The scanty number of patients who suffer the disease, does that the course and treatment of the same one is not known for many specialists, in spite of the importance of the multidisciplinary managing of these patients. We present 2 cases evaluated by our service in the last 12 months; two 40 and 23-year-old males diagnosed in childhood with ossificans progressive fibrodysplasia who attended the maxilofacial surgery department for evaluation and treatment (AU)
Full text:
Available
Collection:
National databases
/
Spain
Database:
IBECS
Main subject:
Oral Surgical Procedures
/
Myositis Ossificans
Type of study:
Etiology study
/
Risk factors
Limits:
Adult
/
Humans
/
Male
Language:
Spanish
Journal:
Rev. esp. cir. oral maxilofac
Year:
2014
Document type:
Article
Institution/Affiliation country:
Hospital Universitario Ramón y Cajal/España