Resonancia magnética de cuerpo entero en un caso de neuroblastoma abdominal oculto con síndrome opsoclonus-myoclonus / Whole-body magnetic resonance imaging in a patient with an occult abdominal neuroblastoma and opsoclonus-myoclonus syndrome
Radiología (Madr., Ed. impr.)
; 56(6): e54-e57, nov.-dic. 2014.
Article
in Spanish
| IBECS
| ID: ibc-129934
Responsible library:
ES1.1
Localization: BNCS
RESUMEN
El síndrome opsoclonus-myoclonus es un trastorno neurológico raro. En la infancia su etiología es variable, aunque en un 40-80% de los casos se trata de una manifestación paraneoplásica, principalmente del neuroblastoma. Con un algoritmo diagnóstico controvertido en la búsqueda de un posible tumor primario, la resonancia magnética de cuerpo entero se vislumbra como una poderosa herramienta. Presentamos el caso de un varón de 2 años con manifestaciones de un síndrome opsoclonus-myoclonus al que se detectó un neuroblastoma retroperitoneal mediante esta técnica de imagen (AU)
ABSTRACT
Opsoclonus-myoclonus syndrome is a rare neurological disorder. In children, the etiology varies, although it is a paraneoplastic manifestation (mainly of neuroblastoma) in 40% to 80% of cases. Whole-body MRI promises to be a powerful tool in the search for a possible primary tumor in this condition for which the diagnostic algorithm is yet to be established. We present the case of a two-year-old boy with signs of opsoclonus-myoclonus syndrome in whom a retroperitoneal neuroblastoma was detected by whole-body MRI (AU)
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Collection:
National databases
/
Spain
Database:
IBECS
Main subject:
Magnetic Resonance Imaging
/
Magnetic Resonance Spectroscopy
/
Abdominal Neoplasms
/
Neuroblastoma
Limits:
Child, preschool
/
Humans
/
Male
Language:
Spanish
Journal:
Radiología (Madr., Ed. impr.)
Year:
2014
Document type:
Article
Institution/Affiliation country:
Hospital Universitario Virgen de las Nieves/España