Hemosiderosis pulmonar idiopática: a propósito de dos casos / Idiopathic pulmonary hemosiderosis: base don two cases
Rev. esp. pediatr. (Ed. impr.)
; 72(4): 201-206, jul.-ago. 2016. tab, ilus
Article
in Spanish
| IBECS
| ID: ibc-156763
Responsible library:
ES1.1
Localization: BNCS
RESUMEN
La hemosiderosis pulmonar idiopática es una enfermedad muy poco frecuente, de inicio fundamentalmente en edad pediátrica. A pesar de su baja incidencia, debemos tenerla en cuenta ante un caso de anemia microcítica ferropénica persistente, a la que se asocie sintomatología respiratoria. El diagnóstico es de sospecha, apoyándonos en la radiología, siendo fundamental el lavado broncoalveolar y la exclusión de otras causas de hemorragia alveolar difusa. Revisamos los aspectos clínicos, diagnósticos y terapéuticos a propósito de 2 casos de esta entidad (AU)
ABSTRACT
Idiopathic pulmonary hemosiderosis is an infrequent disease, with debut mainly in childhood. In spite of its low incidence, we should consider this disease in case of persistent microcytic iron deficiency anemia, with respiratory symptoms associated. The diagnosis is supported by the combination of compatible clinical and radiologycal findings, the ending of hemosiderin-laden alveolar macrophages on the broncoalveolar lavage, and is essential to exclude other causes of alveolar haemorrhage. The diagnostic and therapeutic features are reviewed after the presentation of two clinical cases of this entity (AU)
Full text:
Available
Collection:
National databases
/
Spain
Database:
IBECS
Main subject:
Asthenia
/
Methylprednisolone
/
Bronchoalveolar Lavage
/
Airway Obstruction
/
Hemosiderosis
Type of study:
Diagnostic study
Limits:
Child, preschool
/
Female
/
Humans
/
Male
Language:
Spanish
Journal:
Rev. esp. pediatr. (Ed. impr.)
Year:
2016
Document type:
Article
Institution/Affiliation country:
Complejo Hospitalario de Navarra B/España