Hechos y controversias en la enfermedad mixta del tejido conectivo / Facts and controversies in mixed connective tissue disease
Med. clín (Ed. impr.)
; 150(1): 26-32, ene. 2018. ilus, tab
Article
in Spanish
| IBECS
| ID: ibc-169657
Responsible library:
ES1.1
Localization: BNCS
RESUMEN
La enfermedad mixta del tejido conectivo (EMTC) es una enfermedad reumática autoinmunitaria sistémica (ERAS) caracterizada por la asociación de manifestaciones clínicas de lupus eritematoso sistémico (LES), esclerosis sistémica cutánea (ESC) y polimiositis-dermatomiositis en presencia de títulos elevados de anticuerpos anti-U1-RNP en el suero de los pacientes. Sus principales síntomas son la poliartritis, el edema de manos, el fenómeno de Raynaud, la esclerodactilia, la miositis y la hipomotilidad esofágica. Actualmente, la mayoría de los autores acepta que la EMTC es una entidad independiente, pero algunos mantienen que estos pacientes podrían presentar una ERAS, definida en su fase precoz como LES o ESC, o ser, en realidad, un síndrome de solapamiento de la ERAS (AU)
ABSTRACT
Mixed connective tissue disease (MCTD) is a systemic autoimmune rheumatic disease (SARD) characterised by the combination of clinical manifestations of systemic lupus erythematosus (SLE), cutaneous systemic sclerosis (SSc) and polymyositis-dermatomyositis, in the presence of elevated titers of anti-U1-RNP antibodies. Main symptoms of the disease are polyarthritis, hand oedema, Raynaud's phenomenon, sclerodactyly, myositis and oesophageal hypomobility. Although widely discussed, most authors today accept MCTD as an independent entity. Others, however, suggest that these patients may belong to subgroups or early stages of certain definite connective diseases, such as SLE or SSc, or are, in fact, SARD overlap syndromes (AU)
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Collection:
National databases
/
Spain
Health context:
SDG3 - Health and Well-Being
Health problem:
Target 3.4: Reduce premature mortality due to noncommunicable diseases
Database:
IBECS
Main subject:
Ribonucleoprotein, U1 Small Nuclear
/
Mixed Connective Tissue Disease
Type of study:
Diagnostic study
Limits:
Humans
Language:
Spanish
Journal:
Med. clín (Ed. impr.)
Year:
2018
Document type:
Article
Institution/Affiliation country:
Hospital General Universitario Gregorio Marañón/España
/
Hospital Gregorio Marañón/España
/
Universidad Complutense de Madrid/España