Mesenteritis esclerosante relacionada con IgG4, una entidad rara causante de dolor abdominal / IgG4-related sclerosing mesenteritis, a rare condition that causes abdominal pain
Rev. esp. enferm. dig
; 110(3): 201-203, mar. 2018. ilus
Article
in Spanish
| IBECS
| ID: ibc-171526
Responsible library:
ES1.1
Localization: BNCS
RESUMEN
La distinción de la enfermedad relacionada con IgG4 como una entidad inmunomediada que engloba patologías consideradas clásicamente como idiopáticas ha supuesto una revolución en el algoritmo diagnóstico y terapéutico en diferentes especialidades médicas. Esta entidad suele implicar a diversos órganos (la afectación de un órgano aislado, a excepción del páncreas, es infrecuente), lo cual determina unos hallazgos histopatológicos característicos. Presentamos el caso de un paciente valorado por dolor abdominal que, tras estudio exhaustivo y habiendo descartado otras etiologías, fue diagnosticado de mesenteritis esclerosante IgG4 cumpliendo criterios radiológicos e histopatológicos (AU)
ABSTRACT
The identification of IgG4-related disease as a distinct immune-mediated condition encompassing disorders that were traditionally seen as idiopathic has been a revolution in the diagnostic and therapeutic algorithm in several medical fields. This condition usually involves multiple organs (isolated organ involvement is uncommon except in the pancreas) with characteristic histopathological findings. We report a case that was assessed due to abdominal pain and subsequently diagnosed with IgG4-related sclerosing mesenteritis. A comprehensive work-up of the case ruled out other conditions and a diagnosis of IgG4-related sclerosing mesenteritis was made according to radiographic and histopathological criteria (AU)
Full text:
Available
Collection:
National databases
/
Spain
Database:
IBECS
Main subject:
Adrenal Cortex Hormones
/
Hypergammaglobulinemia
/
Mesentery
Type of study:
Etiology study
/
Prognostic study
Limits:
Adult
/
Humans
/
Male
Language:
Spanish
Journal:
Rev. esp. enferm. dig
Year:
2018
Document type:
Article
Institution/Affiliation country:
Hospitales Universitarios Virgen del Rocío/España