Masa retroperitoneal gigante en el tumor periférico de la vaina neural asociado a neurofibromatosis tipo 1. Reporte de un caso y revisión de la literatura / Giant retroperitoneal mass in peripheral neural sheath tumor associated with neurofibromatosis type 1. Case report and review of the literature
Rev. esp. investig. quir
; 23(1): 31-33, 2020. ilus
Article
in Es
| IBECS
| ID: ibc-191770
Responsible library:
ES1.1
Localization: BNCS
RESUMEN
Los tumores malignos de vaina neural periférica (MPNST) se observan con mayor frecuencia en pacientes con neurofibromatosis tipo 1 (NF-1), presentando un crecimiento rápido y unas tasas de supervivencia a los 5 años alrededor del 33%. Presentamos el caso de un varón de 17 años afecto de NF-1 con un MPNST retroperitoneal gigante sometido a tratamiento quirúrgico radical, con recidiva tumoral precoz
ABSTRACT
Malignant peripheral nerve sheath tumors (MPNST) are most frequently in patients with neurofibromatosis type 1 (NF-1), with a rapid growth and 5-years survival rates around 33%. We present the case of a 17 years old male with NF-1 and a giant retroperi-toneal MPNST who undergoes a radical surgical treatment, with early tumor recurrence
Full text:
1
Collection:
06-national
/
ES
Database:
IBECS
Main subject:
Retroperitoneal Neoplasms
/
Neurofibromatosis 1
Limits:
Adolescent
/
Humans
/
Male
Language:
Es
Journal:
Rev. esp. investig. quir
Year:
2020
Document type:
Article