Nevo sebáceo de Jadassohn. Localización atípica y síndromes asociados / Nevus sebaceus of Jadassohn. Atypical location and associated syndromes
Pediatr. aten. prim
; 25(99)3 oct. 2023. ilus
Article
in Spanish
| IBECS
| ID: ibc-226238
Responsible library:
ES1.1
Localization: ES15.1 - BNCS
RESUMEN
Hamartoma benigno que puede aparecer desde el nacimiento. Se localiza sobre todo en cuero cabelludo y cara; origina una placa alopécica, amarillenta, de superficie rugosa. Tiene tres etapas, una de hiperplasia epidérmica, luego una puberal con desarrollo de glándulas sebáceas y una tardía con desarrollo de tumores benignos o malignos, en especial siringocistadenoma papilífero y tricoblastomas. Puede presentarse asociado a síndromes genéticos. Su exéresis quirúrgica es objeto de controversia (AU)
ABSTRACT
Benign hamartoma that can appear from birth. It is located mainly on the scalp and face; It causes an alopecic, yellowish plaque with a rough surface. It has three stages, one of epidermal hyperplasia, then a pubertal stage with development of sebaceous glands, and a late stage with development of benign or malignant tumors, especially papillary syringocystadenoma and trichoblastoma. It can appear associated with genetic syndromes. Its surgical excision is controversial. (AU)
Full text:
Available
Collection:
National databases
/
Spain
Database:
IBECS
Main subject:
Nevus, Sebaceous of Jadassohn
/
Infant, Newborn, Diseases
Limits:
Humans
/
Male
/
Infant, Newborn
Language:
Spanish
Journal:
Pediatr. aten. prim
Year:
2023
Document type:
Article
Institution/Affiliation country:
Hospital General Universitario de Castellón/España