Amiloidose sistémica associada a mielomamúltiplo / Systemic amyloidosis multiple myeloma-associated
Med. cután. ibero-lat.-am
; 36(2): 84-87, mar.-abr. 2008. tab, ilus
Article
in Portuguese
| IBECS
| ID: ibc-60918
Responsible library:
ES1.1
Localization: BNCS
RESUMO
A amiloidose AL é uma doença que resulta da deposição tecidual de cadeias leves de imunoglobulinas, ocorrendo em 15% dos doentes com mielomamúltiplo. As manifestações mucocutâneas frequentemente antecedem o aparecimento de outros sintomas de gamapatia monoclonal, possibilitandoum diagnóstico mais precoce.Descrevemos o caso de um doente de 71 anos que recorreu à consulta por lesões cutâneas nas pálpebras, sulcos retroauriculares e dorso, cuja biópsiarevelou depósitos amilóides. A investigação subsequente identificou a existência de mieloma múltiplo (AU)
ABSTRACT
AL amyloidosis results from tissue deposition of immunoglobulin light chains, occurring in 15% of patients with multiple myeloma. Mucocutaneouslesions are often the first manifestations, helping in earlier recognition of monoclonal gamapathy.A 71-year-old man who with cutaneous lesions on the eyelids, retroauricular folds and upper back, which proved to be due to amyloid deposition isreported. Further investigation revealed multiple myeloma (AU)
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Collection:
National databases
/
Spain
Database:
IBECS
Main subject:
Amyloidosis
/
Multiple Myeloma
Type of study:
Prognostic study
/
Risk factors
Limits:
Aged
/
Humans
/
Male
Language:
Portuguese
Journal:
Med. cután. ibero-lat.-am
Year:
2008
Document type:
Article
Institution/Affiliation country:
Hospital Garcia de Orta/Portugal