Sarcoidosis sistémica necrotizante con afectación pulmonar y del sistema nervioso central / Necrotizing systemic sarcoidosis with pulmonary and central nervous system involvement
An. med. interna (Madr., 1983)
; 25(1): 23-26, ene. 2008. ilus
Article
in Es
| IBECS
| ID: ibc-62976
Responsible library:
ES15.1
Localization: ES15.1 - BNCS
RESUMEN
La sarcoidosis es una enfermedad sistémica que se diagnostica con la presencia de granulomas no necrotizantes en una biopsia. Sin embargo, hay variantes como la sarcoidosis con granulomas necrotizantes o la sarcoidosis nodular en las que pueden aparecer zonas de necrosis que hacen que el diagnóstico diferencial con procesos infecciosos sea especialmente difícil. Describimos un caso de un paciente, con afectación pulmonar y de lSNC, en quien la presencia de granulomas necrotizantes hizo orientar el diagnóstico inicialmente hacia una tuberculosis con el consiguiente retardo en la instauración del tratamiento específico
ABSTRACT
Sarcoidosis is a multisystemic disease which diagnosis depends on the presence of non necrotizing granulomas in the biopsy. However there are variants such as necrotizing sarcoidal granulomas or nodular sarcoidosis which have atypical findings and make difficult the differential diagnosis with other infectious processes. We describe a case of a man who develops granulomas with extensive necrosis in a systemic sarcoidosis that affected the lung and the central nervous system. This finding made us to make the diagnosis of tuberculosis and delay the specific treatment
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Collection:
National databases
/
Spain
Health context:
Neglected Diseases
Health problem:
Neglected Diseases
/
Tuberculosis
Database:
IBECS
Main subject:
Azathioprine
/
Tuberculosis
/
Vasculitis
/
Central Nervous System
/
Vertigo
/
Sarcoidosis, Pulmonary
/
Diagnosis, Differential
/
Granuloma
/
Immunosuppressive Agents
Type of study:
Diagnostic study
Limits:
Adult
/
Humans
/
Male
Language:
Spanish
Journal:
An. med. interna (Madr., 1983)
Year:
2008
Document type:
Article
Institution/Affiliation country:
Hospital Clínico San Cecilio/España