Arrugamiento acuagénico palmar en unniño con fibrosis quística / Aquagenic wrinkling of the palmas in a young boy with cystic fibrosis
Med. cután. ibero-lat.-am
; 37(3): 139-143, mayo-jun. 2009. ilus, tab
Article
in Spanish
| IBECS
| ID: ibc-80733
Responsible library:
ES1.1
Localization: BNCS
RESUMEN
El arrugamiento acuagénico es una afección cutánea descrita en la última década. Se considera poco frecuente, característico de mujeres jóvenes eidiopático; aunque en al menos tres enfermos se ha relacionado con la toma de antiinflamatorios inhibidores selectivos de la ciclooxigenasa-2. Recientementese ha recuperado su vinculación, realizada hace más de 30 años, con la fibrosis quística, y se ha referido en tres pacientes con dicha enfermedad.Describimos un nuevo caso en un niño de 5 años con fibrosis quística, documentada con estudio genético. Discutimos su eventual consideracióncomo marcador cutáneo de la fibrosis quística (AU)
ABSTRACT
Aquagenic wrinkling is a cutaneous condition described in the last decade. It is considered to be uncommon, typical in young females and idiopathic;although it has been related with selective inhibitor of cyclooxygenasa-2 anti-inflammatory medication intake in at least three patients. Recently itsrelationship with cystic fibrosis, recognised more than 30 years earlier, has been recovered and three patients have been reported in with that disease.A new genetically documented cystic fibrosis case in a 5 year old boy is described. The eventual consideration of this condition as a cystic fibrosis cutaneousmarker is discussed (AU)
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Collection:
National databases
/
Spain
Database:
IBECS
Main subject:
Cystic Fibrosis
/
Keratoderma, Palmoplantar, Epidermolytic
Limits:
Child, preschool
/
Humans
/
Male
Language:
Spanish
Journal:
Med. cután. ibero-lat.-am
Year:
2009
Document type:
Article
Institution/Affiliation country:
Universidad Autónoma/España