Elastosis perforante serpiginosa en pacientes con síndrome de Down / Elastosis perforans serpiginosa in patients with Downs syndrome
Med. cután. ibero-lat.-am
; 38(6): 234-237, nov.-dic. 2010. ilus, tab
Article
in Spanish
| IBECS
| ID: ibc-97229
Responsible library:
ES1.1
Localization: BNCS
RESUMEN
La elastosis perforante serpiginosa es una dermatosis infrecuente de etiología desconocida, caracterizada por la eliminación transepidérmica de fibras elásticas anormales. El síndrome de Down se ha descrito asociado a múltiples dermatosis algunas comunes y otras tan infrecuentes como la elastosis perforante serpiginosa. Describimos dos mujeres con síndrome de Down y elastosis perforante serpiginosa. Revisamos las características peculiares de la elastosis perforante serpiginosa en los pacientes con síndrome de Down y los mecanismos etiopatogénicos posiblemente implicados en su aparición (AU)
ABSTRACT
Elastosis perforans serpiginosa is an infrequent skin dermatosis of unknown aetiology characterized by the transepidermal elimination of abnormal elastic fibres. An increased prevalence of common skin conditions and other peculiar and rare dermatosis such as elastosis perforans serpiginosa has been described in Down´s syndrome. We report here in two women with Down´s syndrome, and elastosis perforans serpiginosa. We review the previous reports of elastosis perforans serpiginosa, the peculiar findings in patients with Down´s syndrome, and possible pathogenetic mechanisms (AU)
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Collection:
National databases
/
Spain
Database:
IBECS
Main subject:
Down Syndrome
/
Elastic Tissue
Type of study:
Diagnostic study
/
Risk factors
Limits:
Female
/
Humans
Language:
Spanish
Journal:
Med. cután. ibero-lat.-am
Year:
2010
Document type:
Article
Institution/Affiliation country:
Universidad de Cantabria/España