Displasia arritmogénica de ventrículo derecho: opciones de tratamiento durante 12 años de seguimiento en un caso / Arrhythmogenic right ventricular dysplasia: Therapeutic options during 12 years follow up in 1 case

ABSTRACT

The replacement of muscle by fibrous and adipose tissue leads to arrhythmogenic right ventricular dyaplasia. We report the clinical features and therapeutic options of a 50 years old male with the disease followed during 12 years. The latter included pharmacological therapy, surgical pseudoaneurysmal resection and radiofrequency fulguration of a second arrhythmogenic focus that appeared 10 after the surgical procedure. The patient remained asymptomatic after each therapy, until the disease progressed again. This follow up is one of the longest reported and documents the disease's clinical presentation, evolution and treatment