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Síndrome de Brown-Vialleto-van Laere: relato de dois casos / Brown-Vialleto-van Laere syndrome: report of 2 cases
Arq. neuropsiquiatr ; 53(4): 789-91, dez. 1995.
Article in Portuguese | LILACS | ID: lil-161586
Responsible library: BR1.1
RESUMO
A síndrome de Brown-Vialleto-van Laere é entidade degenerativa hereditária ou esporádica, rara, caracterizada por surdez neuro-sensorial seguida ou acompanhada por uma variedade de alteraçoes de nervos cranianos, podendo ainda ocorrer acometimento de corno anterior e vias ópticas. Relatamos dois casos de discutimos o diagnóstico diferencial da síndrome com as atrofias espinhais e surdez hereditária.
Subject(s)
Full text: Available Collection: International databases Database: LILACS Main subject: Bulbar Palsy, Progressive / Deafness Limits: Adolescent / Child / Female / Humans / Male Language: Portuguese Journal: Arq. neuropsiquiatr Journal subject: Neurology / Psychiatry Year: 1995 Document type: Article / Congress and conference
Full text: Available Collection: International databases Database: LILACS Main subject: Bulbar Palsy, Progressive / Deafness Limits: Adolescent / Child / Female / Humans / Male Language: Portuguese Journal: Arq. neuropsiquiatr Journal subject: Neurology / Psychiatry Year: 1995 Document type: Article / Congress and conference
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