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Distrofia muscular progressiva congênita / Congenital progressive muscular dystrophy
Rev. bras. neurol ; 22(4): 125-8, jul.-ago. 1986. tab
Article in Portuguese | LILACS | ID: lil-36978
Responsible library: BR1.1
RESUMO
Relatam-se 17 casos de distrofia muscular progressiva congênita comprovados pelos exames clínico, eletromiográfico e histopatológico. É dada ênfase ao fenômeno das retraçöes fibrotendinosas que constituem uma característica fundamental da afecçäo. Ainda mal estudada, a moléstia näo constitui uma entidade bem definida, podendo inclusive afetar as funçöes cerebrais
Subject(s)
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Collection: International databases Database: LILACS Main subject: Muscular Dystrophies Limits: Adolescent / Child / Child, preschool / Female / Humans / Infant / Male / Infant, Newborn Language: Portuguese Journal: Rev. bras. neurol Journal subject: Neurology Year: 1986 Document type: Article
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Collection: International databases Database: LILACS Main subject: Muscular Dystrophies Limits: Adolescent / Child / Child, preschool / Female / Humans / Infant / Male / Infant, Newborn Language: Portuguese Journal: Rev. bras. neurol Journal subject: Neurology Year: 1986 Document type: Article
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