Amiloidose ganglionar mediastinal em paciente com sarcoidose / Mediastinal lymph node amyloidosis in a patient with sarcoidosis
J. bras. pneumol
; 33(2): 222-225, mar.-abr. 2007. ilus
Article
in Portuguese
| LILACS
| ID: lil-459294
Responsible library:
BR1.1
RESUMO
Paciente masculino, 27 anos, com sintomas respiratórios, linfonodomegalia cervical anterior bilateral e hepatomegalia. Os estudos de imagem evidenciaram linfonodomegalia hilar bilateral e infiltrado pulmonar. O paciente foi submetido a biópsias pulmonar e hepática, que evidenciaram presença de granulomas não caseosos. Também foi submetido à biópsia de linfonodo hilar, que revelou a presença de material amilóide. Os achados clínicos, radiológicos e histopatológicos foram compatíveis com sarcoidose e amiloidose ganglionar. A associação entre sarcoidose e amiloidose é raramente descrita.
ABSTRACT
A 27-year-old male patient presented with respiratory symptoms, bilateral enlargement of the cervical lymph nodes and enlarged liver. In the imaging studies, bilateral enlargement of the hilar nodes was observed, together with pulmonary infiltrate. The patient was submitted to lung and liver biopsies, which revealed noncaseating granulomas. The clinical, radiological and histopathological findings were consistent with sarcoidosis and lymph node amyloidosis. The combination of sarcoidosis and amyloidosis has rarely been reported.
Full text:
Available
Collection:
International databases
Database:
LILACS
Main subject:
Sarcoidosis, Pulmonary
/
Amyloidosis
/
Mediastinal Diseases
Limits:
Adult
/
Humans
/
Male
Language:
Portuguese
Journal:
J. bras. pneumol
Journal subject:
Pulmonary Disease (Specialty)
Year:
2007
Document type:
Article
Affiliation country:
Brazil
Institution/Affiliation country:
Universidade Federal do Paraná/BR