Doença de ménétrier: relato de caso em menina / Ménétrier's disease: a female child case report
Rev. paul. pediatr
; 25(3): 294-296, set. 2007.
Article
in Portuguese
| LILACS
| ID: lil-470790
Responsible library:
BR584.1
RESUMO
OBJETIVO:
Relatar um caso de menina com doença de Ménétrier. DESCRIÇÃO DO CASO Menina de dez anos, admitida com história de vômitos, diarréia, distensão e dor abdominal intermitentes há três dias. A suspeita foi apendicite e a paciente foi submetida à laparotomia, com achado de ascite e adenomegalia mesentérica. No pós-operatório, evoluiu com edema generalizado, ascite e derrame pleural. Os exames complementares e a evolução clínica demonstraram tratar-se de doença de Ménétrier.COMENTÁRIOS:
O quadro clínico e os exames solicitados (alfa-1-antitripsina fecal aumentada, mucosa gástrica tipo fúndica com moderado grau de hiperplasia do epitélio luminal e foveolar e seriografia com hipertrofia do pregueado mucoso gástrico) confirmaram a doença de Ménétrier.ABSTRACT
OBJECTIVE:
To report a case of Ménétrier's disease in a girl. CASE DESCRIPTION A 10-year-old girl was admitted to the hospital with a 3-day history of vomiting, diarrhea, intermittent distension and abdominal pain. Appendicitis was suspected, and patient had a laparotomy which showed only ascites and mesenteric adenomegaly. Generalized edema, ascites and right pleural effusion evolved after the surgery. Menetrier's disease was diagnosed by laboratorial exams and clinical evolution.COMMENTS:
Clinical aspects and the increased fecal alpha-1-antitrypsin associated to gastric mucosa of fundic type with moderate level of hyperplasia of lumina and foveola epithelium and serioscopy with hypertrophy of the plica of gastric mucosa confirmed Ménétrier's disease.
Full text:
Available
Collection:
International databases
Health context:
Neglected Diseases
Health problem:
Diarrhea
Database:
LILACS
Main subject:
Ascites
/
Edema
/
Gastritis, Hypertrophic
/
Hypoproteinemia
Limits:
Child
/
Female
/
Humans
Language:
Portuguese
Journal:
Rev. paul. pediatr
Journal subject:
Pediatrics
Year:
2007
Document type:
Article
Affiliation country:
Brazil
Institution/Affiliation country:
Faculdade de Medicina de São José do Rio Preto/BR
/
Famerp/BR
/
Hospital Cândido Rondon/BR
/
Pontifícia Universidade Católica de São Paulo/BR