Aplasia cutis congénita truncal simétricaasociada a feto papiráceo / Symmetric truncal aplasia cutis congenita associated with papyraceous fetus

RESUMEN

Se presenta el caso de una recién nacida a término, producto de gestación gemelar con feto papiráceo. Sus padres eran no consanguíneos, madre hipotiroidea en uso de levotiroxina, padre aparentemente sano. Al examen presentaba lesiones ulcerativas extensas de bordes bien delimitados, base con tejido de granulación y áreas fibrinoides, distribución en H simétrica de aproximadamente 15 x 10 cm en espalda con extensiones distales hacia muslos y bandas cicatrizales extendidas hacia abdomen anterior. Se consideró el caso de aplasia cutis congénita truncal simétrica asociada a feto papiráceo. Se brindaron cuidados neonatales de incubadora y cuna, el cuidado tópico consistió en mantener el defecto húmedo (suero fisiológico) y aséptico (mupirocina ungüento en compresas) logrando el cierre progresivo del mismo, que se completó a los 60 días de vida.

ABSTRACT

We report the case of a female newborn, product of a twin gestation with a papyraceous fetus. Her parents were nonconsanguineous, mother had hypothyroidism treated with levothyroxine, father was apparently healthy. On examination the patient presented extensive ulcerative lesions with clear borders, base with granulation tissue and fibrinoid areas, symmetric distribution in H shape of approximately 15 x 10 cm involving the back, with distal extensions toward thighs and narrow scar bands toward anterior abdomen. We considered the case as symmetric truncal aplasia cutis congenital associated with a papyraceous fetus. We provided standard neonatal care with incubator, the topic care consisted in maintain the wound moist (saline solution) and aseptic (compresses with mupirocin ointment) achieving the progressive closure of the defect, which was completed after 60 days of life.