Aneurismas das artérias coronárias: uma rara manifestação da doneça renal policística autossômica dominante / Coronary aneurysms: a rare manifestation of autosomal dominant polycystic kidney disease
Rev. bras. cardiol. invasiva
; 18(4): 476-478, dez. 2010. ilus
Article
in Portuguese
| LILACS
| ID: lil-582217
Responsible library:
BR44.1
RESUMO
A doença renal policística autossômica dominante (DRPAD), uma das anormalidades genéticas mais comuns, é responsável por 10 por cento dos casos de insuficiência renal crônica terminal. O acometimento extrarrenal da DRPAD manifesta-se por cistos no fígado e pâncreas, aneurismas intra e extracranianos, e anormalidades cardíacas valvares, comprometendo a raiz da aorta e as valvas aórtica e mitral. Neste artigo descrevemos o caso de um paciente com aneurisma das artérias coronárias no contexto de outras manifestações sugestivas de DRPAD.
ABSTRACT
Autosomal dominant polycystic kidney disease (ADPKD) is one of the most common genetic abnormalities and is responsible for over 10% of end-stage chronic kidney disease cases. Extrarenal involvement of ADPKD is manifested by liver and pancreatic cysts, intra and extracranial aneurysms and valvular heart disease, involving the aortic root and the aortic and mitral valves. In this article we report a case of a patient with large coronary artery aneurysms in the context of other manifestations suggesting ADPKD.
Full text:
Available
Collection:
International databases
Database:
LILACS
Main subject:
Coronary Aneurysm
/
Polycystic Kidney Diseases
/
Aneurysm
Limits:
Humans
/
Male
Language:
Portuguese
Journal:
Rev. bras. cardiol. invasiva
Journal subject:
Cardiology
/
CIRURGIA GERAL
Year:
2010
Document type:
Article
Affiliation country:
Brazil
Institution/Affiliation country:
Instituto Dante Pazzanese de Cardiologia/BR