Lepra Dimorfa Lepromatosa (Borderline Lepromatosa, BL) / Dimorphous Lepromatous Leprosy (Borderline Lepromatous, BL
Rev. argent. dermatol
; 93(1)ene.-mar. 2012. ilus
Article
in Spanish
| LILACS
| ID: lil-634449
Responsible library:
AR1.2
RESUMEN
Presentamos un caso de lepra dimorfa lepromatosa, en un hombre austríaco radicado en la Argentina desde hace 40 años, que presentaba placas infiltradas monomorfas y asintomáticas en tronco y miembros, sin alteraciones neurológicas periféricas evidentes. La biopsia de una de las lesiones demostró áreas de hiperplasia fibroblástica perineural "en catafilas de cebolla", granulomas en contacto focal con la epidermis, con transgresión del muro de contención y abundantes bacilos ácido-alcohol resistentes, agrupados en la tinción para micobacterias. El paciente respondió adecuadamente a la terapia con dapsona, rifampicina y clofazimina; sin embargo presentó episodio reacciónal tipo 1 o "reversal", que requirió terapia con prednisona por seis meses.
ABSTRACT
A case of Dimorphous Lepromatous Leprosy in an Austrian man, who had been living in Argentina for the past 40 years is reported. He presented asymptomatic, infiltrated, monomorphous plaques in his trunk and limbs, without peripheral neurologic manifestations. A skin biopsy specimen obtained from an infiltrated lesion on the back, demonstrated areas of perineural fibroblastic hyperplasia "onion-cataphylls like", granulomas contacting epidermis with violation of the Grenz zone and numerous grouped acid-fast bacilli demonstrated with the Ziehl-Neelsen stain. The patient responded well to therapy with dapsone, rifampicine, and clofazamine, but presented a type 1 reaction (reversal reaction) which required a six-months prednisone therapy.
Full text:
Available
Collection:
International databases
Health context:
Neglected Diseases
Health problem:
Leprosy
/
Neglected Diseases
Database:
LILACS
Language:
Spanish
Journal:
Rev. argent. dermatol
Journal subject:
Dermatology
Year:
2012
Document type:
Article
Affiliation country:
Argentina
Institution/Affiliation country:
Hospital Dr. Ignacio Pirovano/AR