Frequência elevada de calcinose em dermatomiosite juvenil: estudo de fatores de risco / High frequency of calcinosis in juvenile dermatomyositis: a risk factor study
Rev. bras. reumatol
; 52(4): 549-553, jul.-ago. 2012. tab
Article
in Portuguese
| LILACS
| ID: lil-644628
Responsible library:
BR1.1
RESUMO
OBJETIVO:
Avaliar a frequência de calcinose em pacientes com dermatomiosite juvenil, bem como estudar possíveis fatores de risco para essa manifestação.MÉTODOS:
Revisão de prontuários de 34 pacientes, com ênfase nas características demográficas, clínicas e laboratoriais, tipo de tratamento e adesão, tipo de evolução (monocíclico, crônico e policíclico) e gravidade da doença. Os pacientes foram separados em grupos aqueles que desenvolveram calcinose (até o sexto mês de acompanhamento ambulatorial e após seis meses de acompanhamento) e os que não desenvolveram calcinose. Vinte e sete pacientes fizeram dois exames de capilaroscopia periungueal (CPU), os quais foram considerados alterados quando era encontrado padrão escleroderma.RESULTADOS:
A média de idade de início dos sintomas dos 34 pacientes foi de 6,5 anos, e o tempo até o diagnóstico foi de 1,2 anos. Setenta por cento eram meninas. Metade dos pacientes teve curso monocíclico da doença, e apenas 14,7% tiveram vasculite grave. Quase 90% dos pacientes que realizaram CPU tiveram alteração na primeira avaliação, e 74% tiveram alteração na segunda avaliação, com uma média de 1,6 anos entre as duas. Dezesseis (47,1%) pacientes apresentaram calcinose. Não houve associação entre as variáveis analisadas e o desenvolvimento da calcinose.CONCLUSÃO:
Não conseguimos demonstrar a presença de fatores de risco para calcinose, apesar de termos encontrado uma frequência dessa complicação em cerca de metade dos pacientes com dermatomiosite juvenil.ABSTRACT
OBJECTIVE:
To assess the frequency of calcinosis in patients with juvenile dermatomyositis, and the possible risk factors for that manifestation.METHODS:
Medical record review of 34 patients, with an emphasis on the following characteristics demographic, clinical and laboratory data; type of treatment; adherence to treatment; disease course (monocyclic, chronic and polycyclic); and disease severity. Patients were divided into two groups as follows those who developed calcinosis (up to the sixth month of follow-up and after six months of follow-up) and those who did not develop calcinosis. Twentyseven patients underwent two nailfold capillaroscopies (NFC), which were considered altered when the scleroderma pattern was found.RESULTS:
The mean age of symptom onset of the 34 patients was 6.5 years, the time until diagnosis was 1.2 years, and 70% were females. Half of the patients had a monocyclic disease course, and only 14.7% had severe vasculitis. Almost 90% of the patients undergoing NFC showed a change on the first assessment, 74% showed a change on the second assessment, and the mean interval between both assessments was 1.6 year. Calcinosis was evidenced in 16 (47.1%) patients. No association was observed between the variables analyzed and the development of calcinosis.CONCLUSION:
No risk factors for calcinosis were identified in this study, although that complication was found in half of the patients with juvenile dermatomyositis studied.
Full text:
Available
Collection:
International databases
Database:
LILACS
Main subject:
Calcinosis
/
Dermatomyositis
Type of study:
Etiology study
/
Observational study
/
Prognostic study
/
Risk factors
/
Screening study
Limits:
Child
/
Female
/
Humans
Language:
Portuguese
Journal:
Rev. bras. reumatol
Journal subject:
Rheumatology
Year:
2012
Document type:
Article
Affiliation country:
Brazil