Telangiectasia macularis eruptiva perstans / Macularis telangectasia eruptive perstans

RESUMEN

Las mastocitosis son un grupo de enfermedades caracterizadas por la hiperplasia de mastocitos funcionalmente normales en diferentes tejidos. Se distinguen cuatro formas cutáneas urticaria pigmentosa, mastocitoma solitario, mastocitosis cutánea difusa y telangiectasia macularis eruptiva perstans (TMEP). La TMEP es una forma de mastocitosis de presentación infrecuente en la infancia, que se caracteriza clínicamente por la presencia de máculas eritemato-castañas telangiectásicas. Su pronóstico es favorable y el tratamiento, de requerirlo, es sintomático y de índole estética. Presentamos dos casos inusuales de TMEP en la edad pediátrica

ABSTRACT

Mastocytosis comprise a group of entities characterized by the hyperplasia of normal mastocytes in different tissues. There are four forms of cutaneous mastocytosis urticaria pigmentosa, solitary mastocytoma, diffuse cutaneous mastocytosis and telangiectasia macularis eruptiva perstans (TMEP). The later is an uncommon condition in children with scarce reports in the literature, characterized by disseminated telangiectatic erythematous to brownish macules. It generally has a good prognosis and treatment, if required, consists in the relief of the symptoms when present or may be done because of cosmetic concern. Here we present two unusual cases of TMEP in the infancy