Derrame pleural recorrente na doença de Erdheim-Chester / Recurrent pleural effusion in EErdheim-Chester disease
Rev. para. med
; 27(4)out.-dez. 2013. ilus
Article
in Portuguese
|
LILACS-Express
| LILACS
| ID: lil-712069
Responsible library:
BR1.1
RESUMO
Introdução:
a doença de Erdheim-Chester é uma rara e pouco conhecida histiocitose de células não-Langerhans, quese caracteriza por ser granulomatosa e infiltrativa, com proliferação de histiócitos contendo colesterol. Relato de Casomulher, de 50 anos, apresentando derrame pleural recorrente, além de doença intersticial pulmonar e osteoesclerosede ossos longos, de crânio e face, onde após a realização da imunohistoqímica concluiu-se tratar de Histiocitose decélulas não Langerhans. Considerações finais na literatura pesquisada acerca das causas de derrame pleural, nada foiencontrado sobre a Doença de Erdheim ChesterABSTRACT
Introduction:
The Erdheim-Chester disease is a rare and little known no-cell histiocytosis Langerhans, which ischaracterized by granulomatous tissue infiltration with proliferation of histiocytes containing cholesterol. Case Reportwoman, 50 years presenting recurrent pleural effusion, and interstitial lung disease and osteosclerosis of long bones,skull and face, and after the completion of imunohistoqímica was concluded to be the non-Langerhans cell histiocytosis.Conclusion:
the literature on the causes of pleural effusion, nothing was found on Erdheim Chester
Full text:
Available
Collection:
International databases
Database:
LILACS
Language:
Portuguese
Journal:
Rev. para. med
Journal subject:
Medicine
Year:
2013
Document type:
Article
Affiliation country:
Brazil
Institution/Affiliation country:
Centro Universitário do Pará/BR
/
Hospital de Clínicas Gaspar Viana/BR