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Reversal of Defective Mitochondrial Biogenesis in Limb-Girdle Muscular Dystrophy 2D by Independent Modulation of Histone and PGC-1α Acetylation.
Pambianco, Sarah; Giovarelli, Matteo; Perrotta, Cristiana; Zecchini, Silvia; Cervia, Davide; Di Renzo, Ilaria; Moscheni, Claudia; Ripolone, Michela; Violano, Raffaella; Moggio, Maurizio; Bassi, Maria Teresa; Puri, Pier Lorenzo; Latella, Lucia; Clementi, Emilio; De Palma, Clara.
Affiliation
  • Pambianco S; Department of Biomedical and Clinical Sciences "Luigi Sacco," Università degli Studi di Milano, 20157 Milano, Italy.
  • Giovarelli M; Department of Biomedical and Clinical Sciences "Luigi Sacco," Università degli Studi di Milano, 20157 Milano, Italy.
  • Perrotta C; Department of Biomedical and Clinical Sciences "Luigi Sacco," Università degli Studi di Milano, 20157 Milano, Italy.
  • Zecchini S; Department of Biomedical and Clinical Sciences, Unit of Clinical Pharmacology, University Hospital "Luigi Sacco"-ASST Fatebenefratelli Sacco, National Research Council-Institute of Neuroscience, Università degli Studi di Milano, 20157 Milano, Italy.
  • Cervia D; Department of Biomedical and Clinical Sciences "Luigi Sacco," Università degli Studi di Milano, 20157 Milano, Italy; Department for Innovation in Biological, Agro-food and Forest systems, Università degli Studi della Tuscia, 01100 Viterbo, Italy.
  • Di Renzo I; Department of Biomedical and Clinical Sciences "Luigi Sacco," Università degli Studi di Milano, 20157 Milano, Italy.
  • Moscheni C; Department of Biomedical and Clinical Sciences "Luigi Sacco," Università degli Studi di Milano, 20157 Milano, Italy.
  • Ripolone M; Neuromuscular Unit, Dino Ferrari Centre, IRCCS Foundation Ca' Granda Ospedale Maggiore Policlinico, Università degli Studi di Milano, 20122 Milano, Italy.
  • Violano R; Neuromuscular Unit, Dino Ferrari Centre, IRCCS Foundation Ca' Granda Ospedale Maggiore Policlinico, Università degli Studi di Milano, 20122 Milano, Italy.
  • Moggio M; Neuromuscular Unit, Dino Ferrari Centre, IRCCS Foundation Ca' Granda Ospedale Maggiore Policlinico, Università degli Studi di Milano, 20122 Milano, Italy.
  • Bassi MT; IRCCS Eugenio Medea, 23842 Bosisio Parini, Italy.
  • Puri PL; Epigenetics and Regenerative Pharmacology, IRCCS Fondazione Santa Lucia, 00142 Roma, Italy; Sanford Children's Health Research Center, Sanford Prebys Burnham Medical Discovery Institute, La Jolla, CA 92037, USA.
  • Latella L; Epigenetics and Regenerative Pharmacology, IRCCS Fondazione Santa Lucia, 00142 Roma, Italy; National Research Council-Institute of Translational Pharmacology, 00179 Roma, Italy.
  • Clementi E; Department of Biomedical and Clinical Sciences, Unit of Clinical Pharmacology, University Hospital "Luigi Sacco"-ASST Fatebenefratelli Sacco, National Research Council-Institute of Neuroscience, Università degli Studi di Milano, 20157 Milano, Italy; IRCCS Eugenio Medea, 23842 Bosisio Parini, Italy.
  • De Palma C; Department of Biomedical and Clinical Sciences, Unit of Clinical Pharmacology, University Hospital "Luigi Sacco"-ASST Fatebenefratelli Sacco, National Research Council-Institute of Neuroscience, Università degli Studi di Milano, 20157 Milano, Italy. Electronic address: clara.depalma@unimi.it.
Cell Rep ; 17(11): 3010-3023, 2016 12 13.
Article in En | MEDLINE | ID: mdl-27974213

Full text: 1 Collection: 01-internacional Database: MEDLINE Main subject: Protein Processing, Post-Translational / Muscular Dystrophies, Limb-Girdle / Fatty Acids / Mitochondria Limits: Animals / Humans Language: En Journal: Cell Rep Year: 2016 Document type: Article Affiliation country: Italy

Full text: 1 Collection: 01-internacional Database: MEDLINE Main subject: Protein Processing, Post-Translational / Muscular Dystrophies, Limb-Girdle / Fatty Acids / Mitochondria Limits: Animals / Humans Language: En Journal: Cell Rep Year: 2016 Document type: Article Affiliation country: Italy