Systemic Lupus Erythematosus-related Lung Disease.
Semin Respir Crit Care Med
; 45(3): 386-396, 2024 Jun.
Article
in En
| MEDLINE
| ID: mdl-38547915
ABSTRACT
Systemic Lupus Erythematosus (SLE) is a multifaceted, multisystem autoimmune disorder with diverse clinical expressions. While prevalence reports vary widely, pulmonary involvement accounts for significant morbidity and mortality in SLE. This comprehensive review explores the spectrum of pulmonary disease in SLE, including upper airway manifestations (e.g., laryngeal affection), lower airway conditions (e.g., bronchitis, bronchiolitis, bronchiectasis), parenchymal diseases (e.g., interstitial lung disease, acute lupus pneumonitis, diffuse alveolar hemorrhage), pleural diseases (e.g., serositis, shrinking lung syndrome), and vascular diseases (e.g., pulmonary arterial hypertension, pulmonary embolism, acute reversible hypoxemia syndrome). We discuss diagnostic modalities, treatment strategies, and prognosis for each pulmonary manifestation. With diagnostics remaining a challenge and with the absence of standardized treatment guidelines, we emphasize the need for evidence-based guidelines to optimize patient care and improve outcomes in this complex disease.
Full text:
1
Collection:
01-internacional
Database:
MEDLINE
Main subject:
Lung Diseases
/
Lupus Erythematosus, Systemic
Limits:
Humans
Language:
En
Journal:
Semin Respir Crit Care Med
Journal subject:
TERAPIA INTENSIVA
Year:
2024
Document type:
Article
Affiliation country:
Denmark
Country of publication:
United States