Muscular dystrophy associated with posterior column involvement

ABSTRACT

We have described the occurance in three adult members of one family (two male and one female) of muscular dystrophy, in which the wasting is mainly scapulo-humeral in distribution. The condition was more marked in the male members and clinically resembled Erb's juvenile type except that the male had, in addition, a well marked peripheral neuropathy. The duration of illness in each case was 25, 29 and 32 years respectively. Reference is made to a previous report (Gil, 1933) of a case of muscular dystrophy of 37 years' duration with posterior column degeneration. (AU)