A Case of Juvenile Xanthogranuloma Developed in a Neurofibromatosis Child with Family History / 대한피부과학회지
Korean Journal of Dermatology
; : 547-549, 2008.
Article
in Korean
| WPRIM (Western Pacific)
| ID: wpr-102059
Responsible library:
WPRO
ABSTRACT
Juvenile xanthogranuloma (JXG) is a fibrohistiocytic proliferative disorder predominant in infancy and childhood. It is a benign and transient skin lesion that usually appears in the cephalic area. Recently, the concurrent finding of neurofibromatosis (NF), juvenile chronic myelogenous leukemia (JCML), and JXG has been repeatedly reported. Especially, the family history of NF may represent a risk factor for the development of JCML in patients with NF and in patients with NF and JXG. So, a finding of JXG and NF in infants should alert the physician to a possible development of JCML. We report a case of JXG developed in a neurofibromatosis child with family history.
Full text:
Available
Database:
WPRIM (Western Pacific)
Main subject:
Skin
/
Risk Factors
/
Xanthogranuloma, Juvenile
/
Neurofibromatoses
/
Leukemia, Myelomonocytic, Juvenile
Type of study:
Etiology study
/
Risk factors
Limits:
Child
/
Humans
/
Infant
Language:
Korean
Journal:
Korean Journal of Dermatology
Year:
2008
Document type:
Article