Concurrent renal and hepatic angiomyolipoma with pulmonary involvement in two patients with tuberous sclerosis / 대한내과학회지
Korean Journal of Medicine
; : 705-709, 2010.
Article
in Korean
| WPRIM (Western Pacific)
| ID: wpr-108495
Responsible library:
WPRO
ABSTRACT
Tuberous sclerosis (TS) involves multiple organs. Angiomyolipoma of the liver or kidney is one of the clinical manifestations of TS. However, coexistent renal and hepatic angiomyolipoma associated with TS is a rare condition. Pulmonary involvement is extremely rare, and occurs in only 0.1~1% of TS. We report two cases of concurrent renal and hepatic angiomyolipomas with pulmonary involvement in patients with TS. The first case was a 35 year-old woman who showed multiple angiomyolipomas in the liver and both kidneys and cystic parenchymal changes in the lungs. The other case was a 27-year-old woman who showed multiple angiomyolipomas in the liver and both kidneys, and multinodular pulmonary shadows. To the best of our knowledge, this is the first reported case of renal and hepatic angiomyolipomas associated with pulmonary involvement in Korea.
Full text:
Available
Database:
WPRIM (Western Pacific)
Main subject:
Tuberous Sclerosis
/
Lymphangioleiomyomatosis
/
Angiomyolipoma
/
Kidney
/
Korea
/
Liver
/
Lung
Limits:
Adult
/
Female
/
Humans
Country/Region as subject:
Asia
Language:
Korean
Journal:
Korean Journal of Medicine
Year:
2010
Document type:
Article